| Chronic idiopathic myelofibrosis with myeloid metaplasia presenting as refractory ascites. | |
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MedLine Citation:
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PMID: 19785025 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Chronic idiopathic myelofibrosis (CIM) with myeloid metaplasia is a myeloproliferative disorder characterized by leukoerythroblastosis, tear drop erythrocytes, extra-medullary hematopoesis (EMH), and varying degree of myelofibrosis. CIM, presenting as refractory ascites secondary to peritoneal hematopoesis, is extremely rare with only six adult cases reported in literature. This is a report of a child with CIM presenting as refractory ascites as a consequence of EMH in the peritoneum. The patient was treated with intermittent hydroxyurea with favorable response over 3 weeks. The patient was thereafter lost to follow up. |
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Authors:
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Bijoy Patra; Anu Maheshwari; Jagdish Chandra; Satinder Aneja; Shilpi Agarwal; Anita Nangia; Anju Seth |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Pediatric blood & cancer Volume: 54 ISSN: 1545-5017 ISO Abbreviation: Pediatr Blood Cancer Publication Date: 2010 Jan |
Date Detail:
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Created Date: 2009-11-17 Completed Date: 2009-12-17 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 101186624 Medline TA: Pediatr Blood Cancer Country: United States |
Other Details:
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Languages: eng Pagination: 151-3 Citation Subset: IM |
Copyright Information:
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Copyright 2009 Wiley-Liss, Inc. |
Affiliation:
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Department of Pediatrics, Lady Hardinge Medical College, New Delhi, India. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Ascites
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complications,
diagnosis*,
drug therapy Child Chronic Disease Diagnosis, Differential Humans Male Primary Myelofibrosis / complications, diagnosis*, drug therapy Recurrence |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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