Document Detail


Chromosome 22q11.2 deletion syndrome (DiGeorge syndrome/velocardiofacial syndrome).
MedLine Citation:
PMID:  21200182     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Chromosome 22q11.2 deletion syndrome is a common syndrome also known as DiGeorge syndrome and velocardiofacial syndrome. It occurs in approximately 1:4000 births, and the incidence is increasing due to affected parents bearing their own affected children. The manifestations of this syndrome cross all medical specialties, and care of the children and adults can be complex. Many patients have a mild to moderate immune deficiency, and the majority of patients have a cardiac anomaly. Additional features include renal anomalies, eye anomalies, hypoparathyroidism, skeletal defects, and developmental delay. Each child's needs must be tailored to his or her specific medical problems, and as the child transitions to adulthood, additional issues will arise. A holistic approach, addressing medical and behavioral needs, can be very helpful.
Authors:
Donna M McDonald-McGinn; Kathleen E Sullivan
Publication Detail:
Type:  Journal Article; Review    
Journal Detail:
Title:  Medicine     Volume:  90     ISSN:  1536-5964     ISO Abbreviation:  Medicine (Baltimore)     Publication Date:  2011 Jan 
Date Detail:
Created Date:  2011-01-04     Completed Date:  2011-02-01     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  2985248R     Medline TA:  Medicine (Baltimore)     Country:  United States    
Other Details:
Languages:  eng     Pagination:  1-18     Citation Subset:  AIM; IM    
Affiliation:
The Children's Hospital of Philadelphia, Philadelphia, Pennsylvania 19104, USA.
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MeSH Terms
Descriptor/Qualifier:
Animals
Chromosome Deletion
Chromosomes, Human, Pair 22
DiGeorge Syndrome* / diagnosis,  epidemiology,  genetics,  immunology
Disease Models, Animal
Genotype
Humans
Mice
Phenotype
Prevalence

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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