Document Detail

Choristoma of the middle ear: a component of a new syndrome?
MedLine Citation:
PMID:  11347640     Owner:  NLM     Status:  MEDLINE    
CASE REPORT: Salivary choristoma of the middle ear is a rare entity. The authors report the 26th known case, which is unique in several respects: the patient had abnormalities of the first and second branchial arches, as well as the otic capsule and facial nerve in ways not yet reported. Our patient presented with bilateral preauricular pits, conchal bands, an ipsilateral facial palsy, and bilateral Mondini-type deformities. A review of the literature revealed salivary choristomas of the middle ear to be frequently associated with branchial arch abnormalities, most commonly the second, as well as abnormalities of the facial nerve.
REVIEW OF THE LITERATURE: All 25 cases were reviewed and the results reported with respect to clinical presentation, associated abnormalities, operative findings, and hearing results. It has been proposed that choristoma of the middle ear may represent a component of a syndrome along with unilateral hearing loss, abnormalities of the incus and/or stapes, and anomalies of the facial nerve.
CONCLUSION: Eighty-six percent of the reported patients with choristoma have three or four of the four criteria listed to designate middle ear salivary choristoma as part of a syndrome. In the remaining four patients, all of the structures were not assessed.
L M Buckmiller; H A Brodie; K J Doyle; W Nemzek
Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  Otology & neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology     Volume:  22     ISSN:  1531-7129     ISO Abbreviation:  Otol. Neurotol.     Publication Date:  2001 May 
Date Detail:
Created Date:  2001-05-11     Completed Date:  2001-10-11     Revised Date:  2011-08-25    
Medline Journal Info:
Nlm Unique ID:  100961504     Medline TA:  Otol Neurotol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  363-8     Citation Subset:  IM    
Department of Otolaryngology, University of California, Davis Medical Center, Sacramento 95817, USA.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Choristoma / diagnosis*
Ear Diseases / diagnosis*
Ear, Middle*
Hearing Disorders / congenital,  diagnosis
Salivary Gland Diseases / diagnosis*
Tomography, X-Ray Computed

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

Previous Document:  Onset overmasking of a brief amplitude increment in a pure tone and sensorineural hearing impairment...
Next Document:  Effect of smoking on the treatment of vertigo.