Document Detail


Cholesterol reduction by a high-glucose diet in a patient with homozygous familial hypercholesterolemia. A preliminary report.
MedLine Citation:
PMID:  7091159     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Homozygous familial hypercholesterolemia is refractory to standard dietary or drug therapy. Recent studies, however, suggest that a high-carbohydrate/low-fat diet may reduce circulation cholesterol levels in normal or hyperlipidemic subjects. In this regard, we treated a nine year old boy with homozygous familial hypercholesterolemia with a liquid formula diet containing 82 to 90 percent of total calories as glucose. The diet was given as a constant nasogastric infusion or as intermittent daytime drinks followed by a nighttime infusion. Plasma total and low-density lipoprotein cholesterol fell from basal levels of 719 mg/dl and 676 mg/dl to 456 mg/dl and 434 mg/dl, respectively, after one week of therapy. After approximately 14 weeks of treatment, plasma total and low-density lipoprotein cholesterol levels were 311 mg/dl and 277 mg/dl, each representing approximately a 58 percent decrease from basal levels. The fall in circulating cholesterol levels was accompanied by a regression of xanthomatous skin lesions, a rise in plasma insulin levels and no change in plasma glucose or glucagon concentrations. No adverse effects of therapy occurred. We conclude that high-carbohydrate diets may be a safe and effective adjunct in the treatment of homozygous familial hypercholesterolemia.
Authors:
P W Stacpoole; L L Swift; H L Greene; A E Slonim; R K Younger; I M Burr
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Publication Detail:
Type:  Case Reports; Journal Article; Research Support, U.S. Gov't, P.H.S.    
Journal Detail:
Title:  The American journal of medicine     Volume:  72     ISSN:  0002-9343     ISO Abbreviation:  Am. J. Med.     Publication Date:  1982 Jun 
Date Detail:
Created Date:  1982-08-07     Completed Date:  1982-08-07     Revised Date:  2007-11-14    
Medline Journal Info:
Nlm Unique ID:  0267200     Medline TA:  Am J Med     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  889-93     Citation Subset:  AIM; IM    
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MeSH Terms
Descriptor/Qualifier:
Anticholesteremic Agents / therapeutic use
Child
Cholesterol / blood*
Dietary Carbohydrates / administration & dosage,  therapeutic use
Dietary Fats / administration & dosage
Glucose / administration & dosage,  therapeutic use*
Humans
Hyperlipoproteinemia Type II / diet therapy*,  therapy
Intubation, Gastrointestinal
Male
Grant Support
ID/Acronym/Agency:
AM 07061-05/AM/NIADDK NIH HHS; AM 20593-02/AM/NIADDK NIH HHS; HL 23525/HL/NHLBI NIH HHS
Chemical
Reg. No./Substance:
0/Anticholesteremic Agents; 0/Dietary Carbohydrates; 0/Dietary Fats; 50-99-7/Glucose; 57-88-5/Cholesterol

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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