Document Detail

Cholangitis associated with paroxysmal nocturnal hemoglobinuria: another instance of ischemic cholangiopathy?
MedLine Citation:
PMID:  7557105     Owner:  NLM     Status:  MEDLINE    
Ischemia is increasingly recognized as a cause of cholangiopathy. The aim of this study was to report a case of association of paroxysmal nocturnal hemoglobinuria with abrupt-onset cholangiopathy. Anomalies resembling sclerosing cholangitis were documented in a patient suffering from recurrent biliary pain. None of the conditions that have been associated with primary sclerosing cholangitis or other forms of cholangiopathy was present, but shortly thereafter, paroxysmal nocturnal hemoglobinuria occurred. Hepatic vein thrombosis later complicated the course of the disease. Because the fortuitous coincidence of these uncommon conditions is unlikely, this case indicates that paroxysmal nocturnal hemoglobinuria is a cause of ischemic cholangiopathy. Other thrombogenic conditions may also be implicated in some instances of apparently idiopathic cholangiopathy.
D Le Thi Huong; D Valla; D Franco; B Wechsler; A De Gramont; A Auperin; P Godeau
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Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  Gastroenterology     Volume:  109     ISSN:  0016-5085     ISO Abbreviation:  Gastroenterology     Publication Date:  1995 Oct 
Date Detail:
Created Date:  1995-11-03     Completed Date:  1995-11-03     Revised Date:  2007-11-15    
Medline Journal Info:
Nlm Unique ID:  0374630     Medline TA:  Gastroenterology     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  1338-43     Citation Subset:  AIM; IM    
Service de Médecine Interne I, Groupe Hospitalier Pitié-Salpêtrière, Paris, France.
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MeSH Terms
Bile Ducts / blood supply*
Budd-Chiari Syndrome / complications
Cholangitis / etiology*
Hemoglobinuria, Paroxysmal / complications*
Ischemia / complications*

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