Document Detail


Cervical spine stenosis in chondrodysplasia punctata.
MedLine Citation:
PMID:  17909344     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Chondrodysplasia punctata (CDP) is a rare skeletal dysplasia characterized by stippled epiphyses during infancy. The frequency is probably underdiagnosed because of the large heterogeneity in this group. Many genotypic variations exist. Although cervical instability is commonly seen in many skeletal dysplasias, cervical spine stenosis associated with CDP is very rare. We report a boy with phenotypic features of brachytelephalangic chondrodysplasia punctata (BCDP) who had severe cervical spine stenosis successfully corrected by vertebrectomies of C6 and C7 with a fibular strut graft. We discuss the significance of this association.
Authors:
Philippe Violas; Bernard Fraisse; Madeleine Chapuis; Henri Bracq
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of pediatric orthopaedics. Part B     Volume:  16     ISSN:  1473-5865     ISO Abbreviation:  J Pediatr Orthop B     Publication Date:  2007 Nov 
Date Detail:
Created Date:  2007-10-02     Completed Date:  2008-09-25     Revised Date:  2011-10-14    
Medline Journal Info:
Nlm Unique ID:  9300904     Medline TA:  J Pediatr Orthop B     Country:  United States    
Other Details:
Languages:  eng     Pagination:  443-5     Citation Subset:  IM    
Affiliation:
Department of Pediatric Orthopaedic Surgery, Pontchaillou University Hospital, Rennes, France. pviolas@hotmail.com
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MeSH Terms
Descriptor/Qualifier:
Cervical Vertebrae / pathology*,  surgery
Child, Preschool
Chondrodysplasia Punctata, Rhizomelic / complications,  genetics,  pathology*
Decompression, Surgical / methods
Genes, Recessive
Humans
Laminectomy
Magnetic Resonance Imaging
Male
Spinal Cord / pathology*
Spinal Cord Compression / etiology,  pathology,  surgery
Spinal Stenosis / etiology,  pathology*,  surgery

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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