| Cervical disc prolapse in childhood associated with Klippel-Feil syndrome. | |
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MedLine Citation:
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PMID: 11219627 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Klippel-Feil syndrome is characterized by a variable degree of congenital fusion of the cervical spine. It can exist in association with other mesodermal deformities affecting several systems. Symptomatic cervical disc prolapse in the context of the syndrome is well documented in young adults. We present a case of a 5-year-old girl with the syndrome, who presented with mild motor developmental delay and cervical cord compression from a prolapsed C3/4 intervertebral disc, seen on MR scan. She also had posterior elements fused from C-2 to C-4. She improved after cervical discectomy. The presence of degenerative disc disease at such a young age and at a level mechanically protected by posterior element fusion indicates a congenital primary defect, rather than mechanical stress fatigue. |
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Authors:
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G M Allsopp; S Griffiths; S Sgouros |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery Volume: 17 ISSN: 0256-7040 ISO Abbreviation: Childs Nerv Syst Publication Date: 2001 Jan |
Date Detail:
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Created Date: 2001-02-21 Completed Date: 2001-05-17 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 8503227 Medline TA: Childs Nerv Syst Country: Germany |
Other Details:
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Languages: eng Pagination: 69-70 Citation Subset: IM |
Affiliation:
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Department of Neurosurgery, Birmingham Children's Hospital, UK. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Cervical Vertebrae
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abnormalities*,
surgery Child, Preschool Diskectomy Female Humans Intervertebral Disk Displacement / diagnosis*, surgery Klippel-Feil Syndrome / diagnosis*, surgery Magnetic Resonance Imaging Motor Skills Disorders / diagnosis Severity of Illness Index Spinal Cord Compression / diagnosis |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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