Document Detail


Cerebral rhinocele, hydrocephalus, and cleft lip and palate in infants with cardiac fibroma.
MedLine Citation:
PMID:  2250168     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Cardiac transplantation was performed in two infants with unresectable fibromas of the myocardium. In one patient, lip surgery was also required for unilateral cleft lip and palate. At autopsy, communicating hydrocephalus of mild to moderate degree was found in both cases. In the patient with facial clefts, there was also a large, ipsilateral cyst, or rhinocele, of the olfactory lobe. This unusual lesion, which seems to represent a previously unreported malformation, was apparently formed by segmental dilatation of a persistent olfactory ventricle. Cerebral or cranial anomalies are thought to be rare in cases of cardiac fibroma; however, macrocephaly was present in five patients. Furthermore, presenting abnormalities among previously reported cases included hydrocephalus in one case, and cleft lip and palate in another. These and other findings suggest that, at least in some cases, cardiac fibroma is a manifestation of a more extensive developmental disorder.
Authors:
G A de León; N Zaeri; R M Donner; N Karmazin
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of the neurological sciences     Volume:  99     ISSN:  0022-510X     ISO Abbreviation:  J. Neurol. Sci.     Publication Date:  1990 Oct 
Date Detail:
Created Date:  1991-01-15     Completed Date:  1991-01-15     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  0375403     Medline TA:  J Neurol Sci     Country:  NETHERLANDS    
Other Details:
Languages:  eng     Pagination:  27-36     Citation Subset:  IM    
Affiliation:
Department of Neurology, Temple University School of Medicine, Philadelphia, PA.
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MeSH Terms
Descriptor/Qualifier:
Brain / abnormalities*
Cleft Lip / complications*
Cleft Palate / complications*
Female
Fibroma / complications*
Heart Neoplasms / complications*
Humans
Infant
Tuberous Sclerosis / complications

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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