| Cerebral arteriovenous fistula in the Klippel-Trenaunay-Weber syndrome. | |
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MedLine Citation:
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PMID: 2838360 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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A 12-week-old girl presented with cutaneous haemangiomata and hemihypertrophy of the chest and right upper extremity--stigmata of the Klippel-Trenaunay-Weber syndrome. Screening cranial CT-scan followed by cerebral angiogram revealed what is believed to be the first reported occurrence of a cerebral arteriovenous fistula in a patient with this syndrome. Craniotomy and clip application successfully obliterated the fistula. Although rare at present, neurovascular involvement in the Klippel-Trenaunay-Weber syndrome may be found more frequently with the newer non-invasive diagnostic methods for screening these children. Such findings may strengthen the putative classification of this syndrome within the group of primary mesodermal (vascular) phakomatoses. |
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Authors:
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N M Oyesiku; N H Gahm; R L Goldman |
Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Developmental medicine and child neurology Volume: 30 ISSN: 0012-1622 ISO Abbreviation: Dev Med Child Neurol Publication Date: 1988 Apr |
Date Detail:
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Created Date: 1988-07-29 Completed Date: 1988-07-29 Revised Date: 2009-11-11 |
Medline Journal Info:
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Nlm Unique ID: 0006761 Medline TA: Dev Med Child Neurol Country: ENGLAND |
Other Details:
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Languages: eng Pagination: 245-8 Citation Subset: IM |
Affiliation:
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Department of Surgery, University of Connecticut. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Angiomatosis
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complications* Cerebral Angiography Female Humans Infant Intracranial Arteriovenous Malformations / complications*, radiography Klippel-Trenaunay-Weber Syndrome / complications*, radiography Tomography, X-Ray Computed |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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