Document Detail


Cerebral amyloid angiopathy-related hemorrhage in a middle-aged patient with Down's syndrome.
MedLine Citation:
PMID:  19065301     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
A patient with Down's syndrome (DS) died of cerebral hemorrhage at age 52. At autopsy, a large sub-cortical hematoma was present in the right frontal lobe, and microscopic examination showed numerous senile plaques and neurofibrillary tangles in an extensive area of neocortex and also disclosed heavy involvement of vascular walls by amyloid deposition. These senile plaque and vascular amyloid deposits were specifically stained with an antibody to Abeta. His APOE genotype was epsilon4/epsilon4. This is a rare case of DS with cerebral amyloid angiopathy (CAA)-related cerebral hemorrhage. Genetic factors, such as APOE genotype, conceivably determine the risk of vascular rupture in individuals with CAA, even among patients with DS.
Authors:
Ko-Suke Naito; Yoshiki Sekijima; Shu-Ichi Ikeda
Publication Detail:
Type:  Case Reports; Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  Amyloid : the international journal of experimental and clinical investigation : the official journal of the International Society of Amyloidosis     Volume:  15     ISSN:  1744-2818     ISO Abbreviation:  Amyloid     Publication Date:  2008 Dec 
Date Detail:
Created Date:  2008-12-09     Completed Date:  2009-01-28     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9433802     Medline TA:  Amyloid     Country:  United States    
Other Details:
Languages:  eng     Pagination:  275-7     Citation Subset:  IM    
Affiliation:
Department of Medicine (Neurology and Rheumatology), Shinshu University School of Medicine, Matsumoto, Japan. tamame@aurora.ocn.ne.jp
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MeSH Terms
Descriptor/Qualifier:
Amyloid beta-Protein / genetics
Apolipoproteins E / genetics
Cerebral Amyloid Angiopathy, Familial / complications*,  genetics,  pathology
Cerebral Hemorrhage / etiology*,  pathology
Down Syndrome / complications*,  genetics,  pathology
Genotype
Humans
Male
Middle Aged
Chemical
Reg. No./Substance:
0/Amyloid beta-Protein; 0/Apolipoproteins E

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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