Document Detail


Cellular phospholipid and cholesterol efflux in high-density lipoprotein deficiency.
MedLine Citation:
PMID:  12642355     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
BACKGROUND: Prospective studies have examined the relationship between coronary artery disease and low plasma levels of high-density lipoprotein cholesterol (HDL-C). METHODS AND RESULTS: We investigated the causes of hypoalphalipoproteinemia (HypoA; HDL-C <5th percentile) in 64 subjects (12 women and 52 men). Apolipoprotein AI-mediated cellular cholesterol and phospholipid efflux were measured in fibroblasts from HypoA subjects, 9 controls, 2 patients with Tangier disease, and 5 patients with hyperalphalipoproteinemia. A phospholipid efflux defect was defined as <70% of controls. Mean HDL-C was 0.49+/-0.21 mmol/L. Cholesterol and phospholipid efflux correlated strongly (r=0.72, P<0.001). Phospholipid efflux and HDL-C (r=0.64, P<0.001) correlated in HypoA subjects. However, phospholipid or cholesterol efflux was no longer a determinant of HDL-C levels at higher levels (> approximately 1.0 mmol/L) of HDL-C. In HypoA subjects, 4 cases of Tangier disease and 6 of familial HDL deficiency (heterozygous Tangier disease) were identified (10 of 64; 16%). In the remaining 54 subjects, mean lipid efflux was not significantly different from controls and subjects with hyperalphalipoproteinemia. A phospholipid efflux defect was identified in 7 additional HypoA subjects, and a cholesterol efflux defect was detected in 11 subjects. In 2 of these subjects, the ABCA1 gene was ruled out as the cause of the efflux defect, while in 3, the low HDL-C trait segregated with the ABCA1 gene locus. CONCLUSIONS: Lipidation of lipid-poor apolipoprotein AI may not be a major determinant of cholesterol accumulation within more mature HDL particles and increasing cholesterol or phospholipid efflux beyond normal levels may not lead to increase in plasma HDL-C levels. ABCA1 is essential in the initial steps of HDL formation but other plasma events are major modulators of HDL-C levels.
Authors:
Michel Marcil; Rachel Bissonnette; Jérôme Vincent; Larbi Krimbou; Jacques Genest
Related Documents :
14594995 - In vivo modulation of hdl phospholipid has opposing effects on sr-bi- and abca1-mediate...
20683325 - Relative roles of various efflux pathways in net cholesterol efflux from macrophage foa...
10634815 - Clearance of cationized ldl cholesterol from a muscle depot is not enhanced in human ap...
12454275 - On the rate of translocation in vitro and kinetics in vivo of the major oxysterols in h...
9622375 - Factors affecting the landing and feeding responses of the tsetse fly glossina pallidip...
18848945 - Development of nonalcoholic steatohepatitis in insulin-resistant liver-specific s503a c...
Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  Circulation     Volume:  107     ISSN:  1524-4539     ISO Abbreviation:  Circulation     Publication Date:  2003 Mar 
Date Detail:
Created Date:  2003-03-18     Completed Date:  2003-04-10     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  0147763     Medline TA:  Circulation     Country:  United States    
Other Details:
Languages:  eng     Pagination:  1366-71     Citation Subset:  AIM; IM    
Affiliation:
Department of Cardiovascular Genetics, McGill University Health Centre, Montréal, Canada.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
ATP-Binding Cassette Transporters / genetics
Adult
Biological Transport
Cells, Cultured
Cholesterol / metabolism*
Cholesterol, HDL / deficiency*
Female
Fibroblasts / metabolism
Humans
Male
Middle Aged
Mutation
Phospholipids / metabolism*
Tangier Disease / blood,  genetics,  metabolism*
Chemical
Reg. No./Substance:
0/ATP binding cassette transporter 1; 0/ATP-Binding Cassette Transporters; 0/Cholesterol, HDL; 0/Phospholipids; 57-88-5/Cholesterol

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  The VIVA trial: Vascular endothelial growth factor in Ischemia for Vascular Angiogenesis.
Next Document:  Cardiac benefits of fish consumption may depend on the type of fish meal consumed: the Cardiovascula...