| Cavernous lymphangioma of the spleen in a patient with Klippel-Trenaunay-Weber syndrome. | |
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MedLine Citation:
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PMID: 8000113 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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A 31-year-old woman presented with hypertrophy of the left upper extremity and thrombocytopenia. Physical examination revealed splenomegaly, and laboratory investigation revealed thrombocytopenia, elevation of cross-linked fibrin degradation products (XDP), and thrombin-antithrombin III complex (TAT). A diagnosis of Klippel-Trenaunay-Weber (K-T-W) syndrome was established by the dermatologic findings and angiography of the extremities. A splenic cavernous lymphangioma was diagnosed by ultrasonography and angiography, and was confirmed by pathology following splenectomy. Post-operatively, the platelet count increased, and hemostatic parameters normalized. Cavernous lymphangioma is a rare complication of Klippel-Trenaunay-Weber syndrome. Splenectomy proved to be an effective therapy for both cavernous lymphangioma and consumptive coagulopathy in Klippel-Trenaunay-Weber syndrome. |
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Authors:
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M Yamazaki; Y Kawamura; T Ohka; S Katada; K Morita; M Nakagawa; E Kubo; A Kawashima; H Shimizu; K Nobata |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Internal medicine (Tokyo, Japan) Volume: 33 ISSN: 0918-2918 ISO Abbreviation: Intern. Med. Publication Date: 1994 Sep |
Date Detail:
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Created Date: 1995-01-24 Completed Date: 1995-01-24 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 9204241 Medline TA: Intern Med Country: JAPAN |
Other Details:
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Languages: eng Pagination: 574-7 Citation Subset: IM |
Affiliation:
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Department of Internal Medicine (III), Kanazawa University School of Medicine. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adult Disseminated Intravascular Coagulation / etiology, surgery Female Humans Klippel-Trenaunay-Weber Syndrome / complications* Lymphangioma / etiology*, surgery Splenectomy Splenic Neoplasms / etiology*, surgery |
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