Document Detail


A case of congenitally absent left internal carotid artery: vascular malformations in 22q11.2 deletion syndrome.
MedLine Citation:
PMID:  19860531     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Our report is on a Hispanic boy for whom, shortly after birth, clinical suspicion of 22q11.2 deletion syndrome (22q11.2DS) was raised as a result of his characteristic features, including facial dysmorphisms and hypotonia. The 22q11.2DS was confirmed by fluorescence in situ hybridization (FISH), noting a 22q11.2 deletion. Further evaluation revealed complete congenital absence of the left internal carotid artery and focal pachygyria of the left hemisphere. Multiple cardiac and vascular anomalies have been previously described in 22q11 deletion syndrome, but congenital absence of the internal carotid has not been previously reported in the literature. We present a clinical case report in detail of this unique 22q11.2 deletion syndrome associated finding.
Authors:
Matthew D Johnson; Lindell R Gentry; Gregory M Rice; Delora L Mount
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association     Volume:  47     ISSN:  1545-1569     ISO Abbreviation:  Cleft Palate Craniofac. J.     Publication Date:  2010 May 
Date Detail:
Created Date:  2010-04-30     Completed Date:  2010-12-23     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9102566     Medline TA:  Cleft Palate Craniofac J     Country:  United States    
Other Details:
Languages:  eng     Pagination:  314-7     Citation Subset:  D; IM    
Affiliation:
Division of Otolaryngology-Head and Neck Surgery, University of Wisconsin School of Medicine and Public Health, Madison, Wisconsin, USA. mjohnson@uwhealth.org
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / genetics
Carotid Artery, Internal / abnormalities*
Chromosomes, Human, Pair 22*
DiGeorge Syndrome / diagnosis*,  genetics
Diagnosis, Differential
Gene Deletion
Humans
In Situ Hybridization, Fluorescence
Infant
Male

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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