| Cardiac involvement in primary myopathies. | |
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MedLine Citation:
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PMID: 11111138 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Simultaneous or temporarily staggered affection of both the skeletal as well as the cardiac muscle (cardiac involvement, CI) is a frequent finding in primary myopathies (MPs). CI leads to impulse generation defects, impulse conduction defects, thickened myocardium, left ventriculalr hypertrabeculation, dilatation of the cardiac cavities, secondary valve insufficiency, reduction of coronary vasodilative reserve, intracardial thrombus formation, and heart failure with systolic and diastolic dysfunction. CI has been found in Duchenne muscular dystrophy (MD), Becker MD, Emery-Dreifuss MD, facioscapulohumeral MD, sarcoglycanopathies, myotubular congenital MD, myotonic dystrophies type 1 and 2, proximal myotonic myopathy, myoadenylate deaminase deficiency, glycogenosis type II, III, IV, VII and IX, carnitine deficiency, mitochondriopathy, desmin MP, nemaline MP, central core disease, multicore MP, congenital fiber-type disproportion MP, Barth syndrome, McLeod syndrome and Bethlem MP. Patients with any of the above-mentioned myopathies should be cardiologically investigated as soon as their diagnosis is established, since sufficient cardiac therapy improves CI in MPs and since management of these patients is influenced by the degree of CI. |
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Authors:
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J Finsterer; C Stöllberger |
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Publication Detail:
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Type: Journal Article; Review |
Journal Detail:
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Title: Cardiology Volume: 94 ISSN: 0008-6312 ISO Abbreviation: Cardiology Publication Date: 2000 |
Date Detail:
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Created Date: 2001-01-11 Completed Date: 2001-01-11 Revised Date: 2005-11-16 |
Medline Journal Info:
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Nlm Unique ID: 1266406 Medline TA: Cardiology Country: SWITZERLAND |
Other Details:
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Languages: eng Pagination: 1-11 Citation Subset: IM |
Copyright Information:
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Copyright 2000 S. Karger AG, Basel. |
Affiliation:
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Ludwig Boltzmann Institute for Research in Epilepsy and Neuromuscular Disorders, Vienna, Austria. fij@2nr.nkr.magwien.gv.at |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Cardiomyopathies
/
classification,
epidemiology,
etiology* Comorbidity Electrocardiography Humans Magnetic Resonance Imaging Muscular Diseases / classification, complications*, epidemiology Prevalence Prognosis Risk Assessment |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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