Document Detail

Cardiac involvement in congenital myotonic dystrophy.
MedLine Citation:
PMID:  2317405     Owner:  NLM     Status:  MEDLINE    
Seven young patients (mean age 19 years 8 months) with congenital myotonic dystrophy and with defined symptoms at birth were investigated by electrocardiography and echocardiography. None had cardiovascular symptoms. Electrocardiograms or echocardiograms or both were abnormal in all patients. Atrioventricular and intraventricular conduction defects were the most common electrocardiographic abnormalities and were seen in five patients. The echocardiographic examinations showed impaired left ventricular systolic function in one patient. Other echocardiographic findings were a small left ventricle and atrium, minor valve defects, and mitral valve prolapse. This study shows that the heart is often affected in young patients with congenital myotonic dystrophy. The specialised conduction system is often affected and so too is the myocardium, causing impaired systolic function.
H Forsberg; B O Olofsson; A Eriksson; S Andersson
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  British heart journal     Volume:  63     ISSN:  0007-0769     ISO Abbreviation:  Br Heart J     Publication Date:  1990 Feb 
Date Detail:
Created Date:  1990-05-03     Completed Date:  1990-05-03     Revised Date:  2009-11-18    
Medline Journal Info:
Nlm Unique ID:  0370634     Medline TA:  Br Heart J     Country:  ENGLAND    
Other Details:
Languages:  eng     Pagination:  119-21     Citation Subset:  AIM; IM    
Department of Internal Medicine, Central Hospital, Boden, Sweden.
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MeSH Terms
Heart Block / complications
Heart Diseases / complications*
Heart Valve Diseases / complications
Myotonic Dystrophy / complications,  congenital*

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