| Cardiac involvement in congenital myopathy. | |
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MedLine Citation:
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PMID: 4055149 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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We examined cardiac changes in 8 patients (4 men and 4 women, age 21-43 years) with congenital myopathy proven by skeletal muscle biopsy. Of 8 patients, 4 showed cardiac changes, including 1 with cytoplasmic body myopathy (patient 1), 2 with minimal change myopathy (patients 2 and 3) and 1 with nemaline myopathy (patient 4). Patients 1 and 2 showed left ventricular dilatation with severe global hypokinesis of left ventricular wall. These clinical features were quite similar to those of dilated cardiomyopathy and the patients were in NYHA class 3 or 4. Patient 3 had severe mitral regurgitation with mitral valve prolapse. This patient also had a persistent left superior vena cava and hypoplasia of the aorta, and her cardiac function was in NYHA class 3. Patient 4 showed moderate global left ventricular hypokinesis but the left ventricle was not dilated. This patient also had sino-atrial block and type A Wolff-Parkinson-White syndrome. His cardiac function was NYHA class 1. In conclusion, various types of congenital myopathy are associated with cardiac changes which can result in severe congestive heart failure. |
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Authors:
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Y Otsuji; M Osame; C Tei; S Minagoe; A Kisanuki; K Arikawa; K Saito; K Nomoto; T Kashima; H Tanaka |
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Publication Detail:
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Type: Case Reports; Journal Article; Research Support, Non-U.S. Gov't |
Journal Detail:
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Title: International journal of cardiology Volume: 9 ISSN: 0167-5273 ISO Abbreviation: Int. J. Cardiol. Publication Date: 1985 Nov |
Date Detail:
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Created Date: 1985-12-19 Completed Date: 1985-12-19 Revised Date: 2007-11-15 |
Medline Journal Info:
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Nlm Unique ID: 8200291 Medline TA: Int J Cardiol Country: NETHERLANDS |
Other Details:
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Languages: eng Pagination: 311-22 Citation Subset: IM |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adult Arrhythmias, Cardiac / congenital Biopsy Cardiac Output Cardiomyopathies / congenital*, pathology Echocardiography Female Heart Septum / pathology Heart Valve Diseases / congenital Heart Ventricles / pathology Humans Male Microscopy, Electron Middle Aged Muscles / pathology Muscular Diseases / congenital*, pathology Myocardial Contraction |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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