Document Detail


Cardiac abnormalities in the fragile X syndrome.
MedLine Citation:
PMID:  2930667     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Twenty three patients with fragile X syndrome underwent cardiovascular assessment. Echocardiography showed dilatation of the aortic root in 12 (52%) and mitral valve prolapse in five (22%), four of whom had an apical mid-systolic click on auscultation. Patients with fragile X syndrome have cardiac defects similar to those seen in other disorders of connective tissue such as Marfan's syndrome and Ehlers-Danlos syndrome. These, and other somatic features, suggest an underlying connective tissue dysplasia.
Authors:
N Sreeram; C Wren; M Bhate; P Robertson; S Hunter
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  British heart journal     Volume:  61     ISSN:  0007-0769     ISO Abbreviation:  Br Heart J     Publication Date:  1989 Mar 
Date Detail:
Created Date:  1989-05-23     Completed Date:  1989-05-23     Revised Date:  2009-11-18    
Medline Journal Info:
Nlm Unique ID:  0370634     Medline TA:  Br Heart J     Country:  ENGLAND    
Other Details:
Languages:  eng     Pagination:  289-91     Citation Subset:  AIM; IM    
Affiliation:
Department of Paediatric Cardiology, Freeman Hospital, Newcastle upon Tyne.
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Adult
Aged
Aged, 80 and over
Echocardiography
Fragile X Syndrome / complications,  pathology*
Heart Defects, Congenital / complications,  pathology*
Humans
Male
Middle Aged
Sex Chromosome Aberrations / pathology*
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