Document Detail


Bullous pemphigoid associated with Shy-Drager syndrome.
MedLine Citation:
PMID:  9714981     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We report a patient with Shy-Drager syndrome who developed multiple tense blisters mainly on the extremities. Circulating anti-basement membrane zone autoantibodies were detected by the indirect immunofluorescence method. Immunoblot analysis using normal human epidermal extracts demonstrated that this patient's serum reacted only with 230 kD bullous pemphigoid antigen (BPAG1). Concerning the pathoetiology of the association of bullous pemphigoid and Shy-Drager syndrome, we discuss a sequence similarity between BPAG1 and dystonin, a candidate gene for dystonia musculorum.
Authors:
A Okazaki; T Iida; T Muramatsu; T Shirai; K Murata; T Takayanagi
Publication Detail:
Type:  Case Reports; Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  The Journal of dermatology     Volume:  25     ISSN:  0385-2407     ISO Abbreviation:  J. Dermatol.     Publication Date:  1998 Jul 
Date Detail:
Created Date:  1998-09-09     Completed Date:  1998-09-09     Revised Date:  2007-11-15    
Medline Journal Info:
Nlm Unique ID:  7600545     Medline TA:  J Dermatol     Country:  JAPAN    
Other Details:
Languages:  eng     Pagination:  465-8     Citation Subset:  IM    
Affiliation:
Department of Dermatology, Nara Medical University, Japan.
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MeSH Terms
Descriptor/Qualifier:
Autoantibodies / analysis
Autoantigens / genetics,  immunology
Basement Membrane / immunology
Carrier Proteins / genetics,  immunology
Collagen*
Cytoskeletal Proteins / genetics,  immunology
Epidermis / immunology
Fluorescent Antibody Technique, Indirect
Humans
Immunoblotting
Male
Middle Aged
Nerve Tissue Proteins / genetics,  immunology
Non-Fibrillar Collagens*
Pemphigoid, Bullous / complications*,  immunology
Shy-Drager Syndrome / complications*
Chemical
Reg. No./Substance:
0/Autoantibodies; 0/Autoantigens; 0/Carrier Proteins; 0/Cytoskeletal Proteins; 0/DST protein, human; 0/Nerve Tissue Proteins; 0/Non-Fibrillar Collagens; 0/collagen type XVII; 9007-34-5/Collagen

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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