Document Detail


Bruck syndrome.
MedLine Citation:
PMID:  15973030     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The combination of arthrogryposis multiplex congenita and osteogenesis imperfecta is extremely rare. This combination is named Bruck syndrome. A 34 week male baby weighing 1.7 kg at birth was noted to have multiple flexion contractures and pterygia at elbows, wrists and knees, in addition to right foot talipes equinovarus deformity. Postnatally the child developed multiple swellings involving both the upper and lower limbs. A plain radiograph revealed the presence of fractures involving the long bones of the upper and lower limbs. A diagnosis of osteogenesis imperfecta with arthrogryposis multiplex congenita was made, and the patient was labeled as a case of Bruck Syndrome. The aim of this report is to make the readers aware regarding this rare entity and to specifically look for presence of features suggestive of osteogenesis imperfecta when encountered with a neonate born with arthrogryposis multiplex congenita.
Authors:
Vikram Datta; Aditi Sinha; Arvind Saili; Sushma Nangia
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Indian journal of pediatrics     Volume:  72     ISSN:  0973-7693     ISO Abbreviation:  Indian J Pediatr     Publication Date:  2005 May 
Date Detail:
Created Date:  2005-06-23     Completed Date:  2006-07-28     Revised Date:  2009-07-15    
Medline Journal Info:
Nlm Unique ID:  0417442     Medline TA:  Indian J Pediatr     Country:  India    
Other Details:
Languages:  eng     Pagination:  441-2     Citation Subset:  IM    
Affiliation:
Department of Pediatrics, Kalawati Saran Children's Hospital, Lady Hardinge Medical College, New Delhi, India. vikramdatta71@rediff.com
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MeSH Terms
Descriptor/Qualifier:
Arthrogryposis / diagnosis*
Humans
Infant, Newborn
Infant, Premature
Male
Osteogenesis Imperfecta / diagnosis*
Syndrome

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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