Document Detail


Blepharophimosis syndrome: association with colobomatous microphthalmos.
MedLine Citation:
PMID:  7546691     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
OBJECTIVE: To highlight the association of colobomatous microphthalmos with blepharophimosis syndrome. RESULT: We present a case of blepharophimosis syndrome associated with bilateral optic disc, retinochoroidal and iris colobomas, and microphthalmos, in a Caucasian boy. Inheritance in this case was autosomal dominant from the maternal side. CONCLUSION: Colobomatous microphthalmos is an infrequent ocular abnormality in the blepharophimosis syndrome. Ophthalmologists should be aware of this association.
Authors:
L R Lee; T J Sullivan
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Australian and New Zealand journal of ophthalmology     Volume:  23     ISSN:  0814-9763     ISO Abbreviation:  Aust N Z J Ophthalmol     Publication Date:  1995 May 
Date Detail:
Created Date:  1995-11-21     Completed Date:  1995-11-21     Revised Date:  2008-11-21    
Medline Journal Info:
Nlm Unique ID:  8505423     Medline TA:  Aust N Z J Ophthalmol     Country:  AUSTRALIA    
Other Details:
Languages:  eng     Pagination:  145-7     Citation Subset:  IM    
Affiliation:
Oculoplastic Clinic, Royal Children's Hospital, Brisbane, Queensland.
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MeSH Terms
Descriptor/Qualifier:
Child, Preschool
Choroid / abnormalities*
Coloboma / genetics*,  pathology
Eyelid Diseases / genetics*,  pathology
Humans
Iris / abnormalities*
Male
Microphthalmos / genetics*,  pathology
Optic Disk / abnormalities*
Prognosis
Retina / abnormalities*
Syndrome
Vision, Ocular

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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