| Biometric and magnetic resonance imaging assessment of dentofacial abnormalities in a case of Klippel-Trénaunay-Weber syndrome. | |
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MedLine Citation:
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PMID: 14716269 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Klippel-Trénaunay-Weber syndrome is characterized by cutaneous hemangioma, arteriovenous fistulas or varicosities (or both), and unilateral hypertrophy of hard and soft tissues with different localization. Klippel-Trénaunay-Weber syndrome represents a syndrome of interest for those in the fields of oral and maxillofacial radiology and pathology because of the high incidence of compromise of the orofacial area in affected patients. The patient reported here presents with all of the 3 characteristic signs of the syndrome. The somatic and facial hypertrophy is contralateral to angiomata. As revealed through the use of magnetic resonance imaging, the primary component of facial hypertrophy is adipic subcutaneous tissue. Statistical analysis of the dental dimensions revealed that teeth on the hypertrophic side are significantly larger than normal. |
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Authors:
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Efisio Defraia; Tiziano Baccetti; Andrea Marinelli; Isabella Tollaro |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Oral surgery, oral medicine, oral pathology, oral radiology, and endodontics Volume: 97 ISSN: 1079-2104 ISO Abbreviation: Oral Surg Oral Med Oral Pathol Oral Radiol Endod Publication Date: 2004 Jan |
Date Detail:
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Created Date: 2004-01-12 Completed Date: 2004-03-11 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 9508562 Medline TA: Oral Surg Oral Med Oral Pathol Oral Radiol Endod Country: United States |
Other Details:
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Languages: eng Pagination: 127-32 Citation Subset: D; IM |
Affiliation:
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Department of Orthodontics, University of Florence, Italy. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adipose Tissue
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abnormalities Biometry Child Face / abnormalities* Facial Asymmetry / pathology Follow-Up Studies Humans Hyperplasia Hypertrophy Klippel-Trenaunay-Weber Syndrome / pathology* Magnetic Resonance Imaging Male Odontometry Tooth Abnormalities / pathology* |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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