Document Detail


Biliary tract manifestations of the Marfan syndrome.
MedLine Citation:
PMID:  3605039     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The diagnosis of the Marfan syndrome rests on the four criteria of characteristic musculoskeletal, cardiovascular, ocular, and familial features. Biliary tract manifestations have not been described. A case of Marfan syndrome with recurrent biliary obstruction is presented. Endoscopic retrograde cholangiograms presented a grossly ectatic biliary system which is postulated to be an unrecognized manifestation of this syndrome. In addition, the patient developed choledocholithiasis, which may have resulted from biliary stasis secondary to bile duct ectasia. Biliary obstruction developed in the presence and absence of choledocholithiasis, the latter apparently through kinking of the ectatic common bile duct. Obstruction was clinically relieved by biliary endoprosthesis. The presence of a Zenker's diverticulum in this patient, also unreported in the Marfan syndrome, is of incidental interest.
Authors:
A P Merza; M W Raiser
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  The American journal of gastroenterology     Volume:  82     ISSN:  0002-9270     ISO Abbreviation:  Am. J. Gastroenterol.     Publication Date:  1987 Aug 
Date Detail:
Created Date:  1987-08-27     Completed Date:  1987-08-27     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  0421030     Medline TA:  Am J Gastroenterol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  779-82     Citation Subset:  IM    
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MeSH Terms
Descriptor/Qualifier:
Aged
Cholestasis / physiopathology*
Common Bile Duct Diseases / physiopathology*
Female
Gallstones / physiopathology
Humans
Marfan Syndrome / diagnosis,  physiopathology*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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