| Bilateral operculum syndrome in childhood. | |
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MedLine Citation:
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PMID: 19196875 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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We describe 3 patients with bilateral operculum syndrome. They presented with various degrees of suprabulbar (pseudobulbar) signs in addition to delay in cognitive, motor, and speech development in 2 children and developmental language disorder in the third one. A patient with schizencephaly in the left perisylvian area and contralateral polymicrogyria had spastic hemiparesis on the right side, whereas another patient showed bilateral underdevelopment of the opercula in association with axial hypotonia and spastic diplegia. Both of them had epileptiform discharges on the electroencephalogram without clinical manifestations of seizures. The magnetic resonance imaging of the third child with developmental language disorder was normal; however, his electroencephalogram showed frequent bilateral subclinical centrotemporal epileptiform discharges, probably responsible for the speech delay. Structural or functional involvement of the opercula bilaterally was a common finding in all the 3 patients and they had symptoms similar to those described in the developmental type of Foix-Chavany-Marie and Worster-Drought syndromes. |
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Authors:
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Nóra Szabó; Agnes Hegyi; Márta Boda; Margit Páncsics; Csenge Pap; Kristóf Zágonyi; Eva Romhányi; Sándor Túri; László Sztriha |
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Publication Detail:
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Type: Case Reports; Journal Article; Research Support, Non-U.S. Gov't Date: 2009-02-05 |
Journal Detail:
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Title: Journal of child neurology Volume: 24 ISSN: 1708-8283 ISO Abbreviation: J. Child Neurol. Publication Date: 2009 May |
Date Detail:
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Created Date: 2009-05-01 Completed Date: 2009-08-10 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 8606714 Medline TA: J Child Neurol Country: United States |
Other Details:
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Languages: eng Pagination: 544-50 Citation Subset: IM |
Affiliation:
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Department of Paediatrics, University of Szeged, Szeged, Hungary. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Brain
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pathology,
physiopathology Cerebral Palsy / diagnosis, pathology, physiopathology Child Cognition Disorders / diagnosis, pathology, physiopathology Developmental Disabilities / diagnosis, pathology*, physiopathology* Diagnosis, Differential Electroencephalography Epilepsy / diagnosis, pathology, physiopathology Female Frontal Lobe / pathology*, physiopathology* Humans Magnetic Resonance Imaging Male Movement Disorders / diagnosis, pathology, physiopathology Neuropsychological Tests Paresis / diagnosis, pathology, physiopathology Speech Disorders / diagnosis, pathology, physiopathology Syndrome Temporal Lobe / pathology*, physiopathology* |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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