Document Detail

Bielschowsky bodies (Lafora bodies of Bielschowsky type): report of a case associated with Rosenthal fibers in the brain stem.
MedLine Citation:
PMID:  11699566     Owner:  NLM     Status:  MEDLINE    
Bielschowsky bodies are an uncommon type of polyglucosan body. Similar to Lafora bodies, they are characteristically identified within neuronal perikarya and neurites. However, they lack the diffuse distribution of Lafora bodies, and instead are typically restricted to the external pallidum, often in association with status marmoratus or atrophy of the putamen. Fewer numbers of Bielschowsky bodies have also been identified in other areas such as the substantia nigra, putamen and inner globus pallidus. We report an additional case with Bielschowsky bodies in an 18-year old female with cerebral palsy. This case demonstrated multifocal Bielschowsky bodies and abundant Rosenthal fibers in the midbrain and pons. To our knowledge the association of Bielschowsky bodies with this peculiar distribution of Rosenthal fibers has not previously been reported.
J D Wilson; D S Horoupian
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Acta neuropathologica     Volume:  102     ISSN:  0001-6322     ISO Abbreviation:  Acta Neuropathol.     Publication Date:  2001 Nov 
Date Detail:
Created Date:  2001-11-08     Completed Date:  2002-04-16     Revised Date:  2007-11-09    
Medline Journal Info:
Nlm Unique ID:  0412041     Medline TA:  Acta Neuropathol     Country:  Germany    
Other Details:
Languages:  eng     Pagination:  505-9     Citation Subset:  IM    
Department of Pathology, Stanford University, CA 94305, USA.
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MeSH Terms
Athetosis / pathology
Brain / pathology,  ultrastructure
Brain Stem / pathology*
Cerebral Palsy / pathology*
Epilepsy / pathology*
Gliosis / pathology
Inclusion Bodies / pathology*,  ultrastructure
Microscopy, Electron
Middle Aged
Neurons / pathology*,  ultrastructure

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