| Bielschowsky bodies (Lafora bodies of Bielschowsky type): report of a case associated with Rosenthal fibers in the brain stem. | |
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MedLine Citation:
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PMID: 11699566 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Bielschowsky bodies are an uncommon type of polyglucosan body. Similar to Lafora bodies, they are characteristically identified within neuronal perikarya and neurites. However, they lack the diffuse distribution of Lafora bodies, and instead are typically restricted to the external pallidum, often in association with status marmoratus or atrophy of the putamen. Fewer numbers of Bielschowsky bodies have also been identified in other areas such as the substantia nigra, putamen and inner globus pallidus. We report an additional case with Bielschowsky bodies in an 18-year old female with cerebral palsy. This case demonstrated multifocal Bielschowsky bodies and abundant Rosenthal fibers in the midbrain and pons. To our knowledge the association of Bielschowsky bodies with this peculiar distribution of Rosenthal fibers has not previously been reported. |
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Authors:
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J D Wilson; D S Horoupian |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Acta neuropathologica Volume: 102 ISSN: 0001-6322 ISO Abbreviation: Acta Neuropathol. Publication Date: 2001 Nov |
Date Detail:
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Created Date: 2001-11-08 Completed Date: 2002-04-16 Revised Date: 2007-11-09 |
Medline Journal Info:
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Nlm Unique ID: 0412041 Medline TA: Acta Neuropathol Country: Germany |
Other Details:
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Languages: eng Pagination: 505-9 Citation Subset: IM |
Affiliation:
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Department of Pathology, Stanford University, CA 94305, USA. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adolescent Adult Aged Athetosis / pathology Brain / pathology, ultrastructure Brain Stem / pathology* Cerebral Palsy / pathology* Child Epilepsy / pathology* Female Gliosis / pathology Humans Inclusion Bodies / pathology*, ultrastructure Male Microscopy, Electron Middle Aged Neurons / pathology*, ultrastructure |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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