Document Detail

Benign myoclonus of early infancy.
MedLine Citation:
PMID:  10937134     Owner:  NLM     Status:  MEDLINE    
Benign myoclonus of early infancy, first described by Fejerman and Lombroso, is a paroxysmal phenomenon of the first 2 years of life which occurs in neurologically healthy infants during wakefulness, and is usually triggered by excitement or frustration. We studied the neurophysiological features of the phenomenon in five children, aged 7 to 11 months, who were monitored by video-EEG recording, and by polygraphic recording in 3 of the 5 cases. The phenomenon is characterized by a shudder-type, paroxysmal motor manifestation involving mainly the trunk and sometimes the head, associated with tonic limb contractions of variable intensity, from hardly noticeable to more sustained. The EEG counterpart never showed modifications, the polygraphic study demonstrated a brief tonic limb contraction. The clinical manifestation should not be confused with the spasms of epileptic infantile spasms syndrome, or with tonic reflex seizures of early infancy. Although the phenomenon is already widely known, its polygraphic recording is rarely reported in literature. The polygraphic data of our patients contributes to the diagnosis and understanding of the pathophysiology of this paroxysmal manifestation.
C Pachatz; L Fusco; F Vigevano
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Epileptic disorders : international epilepsy journal with videotape     Volume:  1     ISSN:  1294-9361     ISO Abbreviation:  Epileptic Disord     Publication Date:  1999 Mar 
Date Detail:
Created Date:  2000-09-07     Completed Date:  2000-09-07     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  100891853     Medline TA:  Epileptic Disord     Country:  FRANCE    
Other Details:
Languages:  eng     Pagination:  57-61     Citation Subset:  IM    
Neurophysiology Unit, Bambino Gesù Children's Hospital Rome, Italy.
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MeSH Terms
Brain Mapping
Cerebral Cortex / physiopathology
Diagnosis, Differential
Epilepsies, Myoclonic / diagnosis*,  physiopathology
Myoclonus / diagnosis*,  physiopathology
Spasms, Infantile / diagnosis,  physiopathology
Video Recording

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