Document Detail


Basilar impression and platybasia in osteogenesis imperfecta tarda.
MedLine Citation:
PMID:  7071726     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Osteogenesis imperfecta, a rare, genetically transmitted disorder of bone, is known to be associated with the development of basilar impression and platybasia. These deformities of the base of the skull may cause neurosurgical abnormalities secondary to compression of the brainstem and hydrocephalus. The case is presented of a young boy with a family history of osteogenesis imperfecta tarda who suffered respiratory arrest during hospitalization. Cranial nerves and pyramidal tract signs were demonstrated. Roentgenograms showed severe basilar impression and hydrocephalus. Decompression of the brainstem and shunting were performed with improvement in the patient's neurological status. This case represents a rare by significant central nervous system complication of osteogenesis imperfecta. Early recognition and implementation of aggressive treatment are important if irreversible neurological deficits are to be avoided.
Authors:
E Frank; T Berger; J M Tew
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Surgical neurology     Volume:  17     ISSN:  0090-3019     ISO Abbreviation:  Surg Neurol     Publication Date:  1982 Feb 
Date Detail:
Created Date:  1982-06-14     Completed Date:  1982-06-14     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  0367070     Medline TA:  Surg Neurol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  116-9     Citation Subset:  IM    
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Humans
Male
Nervous System Malformations
Osteogenesis Imperfecta / complications*,  radiography
Platybasia / complications*,  radiography

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