Document Detail


Autoimmune polyglandular syndrome type 2 with myasthenia gravis crisis.
MedLine Citation:
PMID:  19901721     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We describe a rare case of autoimmune polyglandular syndrome type 2 initially presenting as Addison disease and autoimmune thyroid disease, with subsequent development of autoimmune hepatitis and myasthenia gravis (MG) crisis in a Japanese woman. MG improved with oral prednisolone followed by plasmapheresis for immunoadsorption; thymectomy was not performed. Conventional treatment for MG was effective and safe in this case, in which there was positivity for human leukocyte antigen A23, B52, B62, DR11, and DR15.
Authors:
Shingo Konno; Takamasa Ichijo; Mayumi Murata; Takahiro Toda; Hiroshi Nakazora; Nobuatsu Nomoto; Hideki Sugimoto; Hiroshi Nemoto; Teruyuki Kurihara; Nobuo Wakata; Toshiki Fujioka
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  The neurologist     Volume:  15     ISSN:  1074-7931     ISO Abbreviation:  Neurologist     Publication Date:  2009 Nov 
Date Detail:
Created Date:  2009-11-10     Completed Date:  2010-01-26     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9503763     Medline TA:  Neurologist     Country:  United States    
Other Details:
Languages:  eng     Pagination:  361-3     Citation Subset:  IM    
Affiliation:
Division of Neurology, and daggerDepartment of Internal Medicine, Division of Diabetes, Toho University Ohashi Medical Center, Tokyo, Japan. d500372@oha.toho-u.ac.jp
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MeSH Terms
Descriptor/Qualifier:
Aged
Female
Glucocorticoids / therapeutic use
Humans
Myasthenia Gravis / complications*,  drug therapy,  surgery
Plasmapheresis / methods
Polyendocrinopathies, Autoimmune / complications*,  drug therapy,  surgery
Prednisolone / therapeutic use
Thymectomy / methods
Chemical
Reg. No./Substance:
0/Glucocorticoids; 50-24-8/Prednisolone

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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