Document Detail

Atypical presentation of extranodal Rosai-Dorfman disease.
MedLine Citation:
PMID:  19161795     Owner:  NLM     Status:  MEDLINE    
We describe a 42-year-old woman with progressive dyspnea on exertion resulting from pulmonary artery compression by a mediastinal mass due to extranodal Rosai-Dorfman disease. After initial biopsies were inconclusive, she underwent surgical resection of the mass to relieve the pulmonary artery compression, which was causing severe right ventricular dysfunction. Debulking of the mass required resection and reconstruction of the ascending aorta, pulmonary trunk, and bilateral pulmonary arteries using cardiopulmonary bypass and circulatory arrest. We believe this is the first report of Rosai-Dorfman disease manifesting as compression of the thoracic great vessels.
Brandon L Prendes; William T Brinkman; Anita L Sengupta; Joseph E Bavaria
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  The Annals of thoracic surgery     Volume:  87     ISSN:  1552-6259     ISO Abbreviation:  Ann. Thorac. Surg.     Publication Date:  2009 Feb 
Date Detail:
Created Date:  2009-01-23     Completed Date:  2009-02-11     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  15030100R     Medline TA:  Ann Thorac Surg     Country:  Netherlands    
Other Details:
Languages:  eng     Pagination:  616-8     Citation Subset:  AIM; IM    
Division of Cardiac Surgery, University of Pennsylvania, Philadelphia, Pennsylvania, USA.
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MeSH Terms
Aorta, Thoracic / pathology*,  surgery
Biopsy, Needle
Cardiopulmonary Bypass
Decompression, Surgical / methods
Follow-Up Studies
Heart Failure / diagnosis,  etiology
Histiocytosis, Sinus / complications,  diagnosis*
Mediastinal Diseases / diagnosis,  pathology*,  surgery
Pulmonary Artery / pathology*,  surgery
Rare Diseases
Risk Assessment
Thoracotomy / methods
Treatment Outcome
Vascular Surgical Procedures / methods

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

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