Document Detail


Atypical facet of Möbius syndrome: association with facioscapulohumeral muscular dystrophy.
MedLine Citation:
PMID:  18059038     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We describe a patient with facioscapulohumeral muscular dystrophy (FSHD) associated with Möbius syndrome and congenital ophthalmoplegia. This 7-year-old girl had profound limitation of extraocular movements since birth, congenital facial diplegia, neonatal hypotonia, and progressive limb-girdle weakness. FSHD genetic testing revealed a pathogenic haplotype with a D4Z4 repeat of 30 kb. The father carries the same allele, although is minimally affected. This unusual case expands the genotypic-phenotypic spectrum of FSHD.
Authors:
Hanna K Kolski; Norma J Leonard; Richard J L F Lemmers; John S Bamforth
Related Documents :
4051868 - Proximal symphalangia and stapes ankylosis.
21331818 - Fatal spontaneous subdural bleeding due to neonatal giant cell hepatitis: a rare differ...
17652228 - Venous ulcers of the lower limbs due to congenital thalidomide-related valve defect.
9167348 - Congenital onychodysplasia of the index fingers--iso-kikuchi syndrome. a case involving...
3242508 - Cockayne syndrome: mri correlates of hypomyelination.
19014058 - Prenatally diagnosed lethal type larsen-like syndrome associated with bifid tongue.
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Muscle & nerve     Volume:  37     ISSN:  0148-639X     ISO Abbreviation:  Muscle Nerve     Publication Date:  2008 Apr 
Date Detail:
Created Date:  2008-03-27     Completed Date:  2008-05-22     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  7803146     Medline TA:  Muscle Nerve     Country:  United States    
Other Details:
Languages:  eng     Pagination:  526-9     Citation Subset:  IM    
Affiliation:
Department of Pediatrics, Aberhart Centre 1, University of Alberta, Edmonton, AB, Canada. Hanna.Kolski@capitalhealth.ca
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Alleles
Blotting, Southern
Child
Diagnosis, Differential
Female
Haplotypes
Humans
Mobius Syndrome / diagnosis*,  genetics*
Muscular Atrophy / diagnosis,  genetics
Muscular Dystrophy, Facioscapulohumeral / diagnosis*,  genetics*
Ophthalmoplegia / diagnosis,  genetics
Pedigree

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  World disparities in risk definition and management of retinoblastoma: a report from the Internation...
Next Document:  Lifetime course of myasthenia gravis.