Document Detail

Atresia of the left atrioventricular valve with patency of the aorta: anatomico-functional analysis of 23 patients.
MedLine Citation:
PMID:  1724232     Owner:  NLM     Status:  MEDLINE    
We analyzed the findings in 23 patients with atresia of the left atrioventricular valve and a patent aorta seen in the period from January 1980 to July 1989. Having divided the cases according to the anatomical findings, we made a subsequent analysis of the clinical and surgical results with the aim of establishing the management most likely to diminish risks, still high, in treatment of this complex anomaly. From the anatomical viewpoint, three variants were observed. In the first, made up of 15 cases, there was absence of the left atrioventricular connexion. The characteristic finding in the second group, with five cases, was an imperforate left atrioventricular valve in the setting of concordant atrioventricular connexions. The third group, of these cases, was dominated by the presence of isomerism of the atrial appendages, both appendages being of left morphology in one case, and of right morphology in the other two. Further anatomical variation was then found in each group. Nine of the 15 with absence of the left atrioventricular connexion had the right atrium connected to a dominant left ventricle in presence of a rudimentary and incomplete right ventricle associated with discordant ventriculo-arterial connexions, all of them being in usual atrial arrangement and three with pulmonary stenosis. The remaining six in this first variant had the right atrium connected to a dominant right ventricle. In the five patients with imperforate left atrioventricular valves, two had discordant and three had concordant ventriculo-arterial connexions. In the three cases with isomerism, two had absence of the left atrioventricular connexion, with a dominant right ventricle. The last patient had an imperforate left atrioventricular valve and a discordant ventriculo-arterial connexion. From the functional viewpoint, there were 14 patients (10 with absence of an atrioventricular connexion, four with imperforate atrioventricular valve) with congestive heart failure and nine patients (five from the first, one from second, and three from the third variant) with hypoxia. Long-term follow-up (median 16.4 months--varying from 1 to 41 months--in the group with congestion and 27.7 months--varying from 12 to 57 months--in those with hypoxia) showed favorable clinical evolution in 11 (91%). We conclude that an anatomico-functional division can point towards the most appropriate management in this complex anomaly.
E Atik; N M Ikari; V D Aiello; A M Albuquerque; E R Iwahashi; M Ebaid; M Barbero-Marcial; A Jatene; F Pileggi
Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  International journal of cardiology     Volume:  32     ISSN:  0167-5273     ISO Abbreviation:  Int. J. Cardiol.     Publication Date:  1991 Sep 
Date Detail:
Created Date:  1992-04-02     Completed Date:  1992-04-02     Revised Date:  2007-11-15    
Medline Journal Info:
Nlm Unique ID:  8200291     Medline TA:  Int J Cardiol     Country:  NETHERLANDS    
Other Details:
Languages:  eng     Pagination:  281-90     Citation Subset:  IM    
Instituto do Coração do Hospital, Universidade de São Paulo, Brasil.
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MeSH Terms
Aorta / pathology*,  physiopathology
Cardiomegaly / physiopathology
Child, Preschool
Follow-Up Studies
Heart Catheterization
Heart Defects, Congenital / pathology,  physiopathology,  surgery
Heart Failure / physiopathology
Infant, Newborn
Mitral Valve / abnormalities*,  pathology,  physiopathology,  surgery,  ultrasonography
Palliative Care
Pulmonary Valve Stenosis / pathology,  physiopathology,  surgery
Retrospective Studies
Survival Rate
Vascular Patency*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

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