Document Detail


Assisted reproductive technology and congenital overgrowth: some speculations on a case of Pallister-Killian syndrome.
MedLine Citation:
PMID:  15378537     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We report on a boy with Pallister-Killian syndrome (PKS) who was conceived by assisted reproductive technology (ART), specifically in vitro fertilization (IVF) with parents' gametes. A prenatal diagnosis performed elsewhere by CVS failed to detect the presence of the isochromosome 12p that was demonstrated postnatally in approximately 50% of cultured skin fibroblasts. Given that the patient did not show the congenital overgrowth typical of PKS, we speculate that ART might have restricted overgrowth in this particular case. More broadly, we hypothesize that overgrowth might protect from early demise fetuses conceived by ART, a technology known to cause low and very low birth weight.
Authors:
P Chiurazzi; J Bajer; E Tabolacci; M G Pomponi; R Lecce; M Zollino; G Neri
Related Documents :
22009007 - Familial hemophagocytic lymphohistiocytosis in 2 siblings with dysmorphogenesis: a new ...
8494307 - Congenital cutis laxa: a case report and review of loose skin syndromes.
21206147 - Huge caudate lobe of the liver due to budd-chiari syndrome.
6872357 - Chemically induced congenital thymic dysgenesis in the rat: a model of the digeorge syn...
19571767 - Hyperkalemia-induced brugada pattern: an unusual manifestation.
7677697 - Cushing syndrome in pregnancy secondary to an adrenal cortical adenoma.
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  American journal of medical genetics. Part A     Volume:  130A     ISSN:  1552-4825     ISO Abbreviation:  Am. J. Med. Genet. A     Publication Date:  2004 Oct 
Date Detail:
Created Date:  2004-09-24     Completed Date:  2005-02-08     Revised Date:  2008-05-21    
Medline Journal Info:
Nlm Unique ID:  101235741     Medline TA:  Am J Med Genet A     Country:  United States    
Other Details:
Languages:  eng     Pagination:  315-6     Citation Subset:  IM    
Affiliation:
Istituto di Genetica Medica, Facoltà di Medicina "A. Gemelli," Università Cattolica del S. Cuore, Roma, Italy.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / genetics,  pathology*
Aneuploidy
Chromosomes, Human, Pair 12 / genetics
Craniofacial Abnormalities
Ear / abnormalities
Fertilization in Vitro
Humans
Infant
Infant, Low Birth Weight*
Infant, Newborn
Karyotyping
Male
Mosaicism
Reproductive Techniques, Assisted*
Syndrome

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Classical West "syndrome" phenotype with a subtelomeric 4p trisomy.
Next Document:  The KBG syndrome: confirmation of autosomal dominant inheritance and further delineation of the phen...