| Arteriohepatic dysplasia: association of liver disease with pulmonary arterial stenosis as well as facial and skeletal abnormalities. | |
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MedLine Citation:
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PMID: 6450397 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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The clinical features and course of five children with the recently described syndrome of arteriohepatic dysplasia are presented. All had bilateral pulmonary arterial stenosis, proven at cardiac catheterization, as well as associated liver disease of varying severity. In one of the fatal cases, a hitherto undescribed anomaly was found--stenosis of the right coronary artery ostium. A viral etiology, eg, the congenital rubella syndrome, was considered most likely, but detailed investigations proved to be negative. |
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Authors:
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S E Levin; P Zarvos; S Milner; A Schmaman |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Pediatrics Volume: 66 ISSN: 0031-4005 ISO Abbreviation: Pediatrics Publication Date: 1980 Dec |
Date Detail:
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Created Date: 1981-03-17 Completed Date: 1981-03-17 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 0376422 Medline TA: Pediatrics Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 876-83 Citation Subset: AIM; IM |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Abnormalities, Multiple*
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complications Bone and Bones / abnormalities* Cardiomegaly / physiopathology Child Child, Preschool Face / abnormalities* Female Growth Disorders / complications Humans Infant Liver / pathology Liver Diseases / complications*, pathology Male Pulmonary Artery / abnormalities* |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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