| Arrhythmia-related workup in hereditary myopathies. | |
| | |
MedLine Citation:
|
PMID: 22424849 Owner: NLM Status: Publisher |
Abstract/OtherAbstract:
|
BACKGROUND: Arrhythmias determine life expectancy in patients with hereditary myopathies. AIMS: The aim of this study was to summarize recent advances in the diagnosis and management of arrhythmias in hereditary myopathies. METHODS: Literature search via PubMed and inclusion of own experiences were performed. RESULTS: All types of arrhythmias can be found in patients with hereditary myopathies, but some are more prevalent than others. Arrhythmias reported in myopathies include atrial fibrillation, atrial flutter, sick-sinus syndrome, preexcitation syndromes, atrioventricular conduction delay, intraventricular conduction delay, and ventricular tachycardia. Sudden cardiac death is a common finding in certain myopathies, and patients at risk for ventricular arrhythmias and sudden cardiac death should be identified early enough to implant a cardioverter-defibrillator to prevent a fatal outcome. Myopathies associated with a high risk for arrhythmias include laminopathies, Emery-Dreifuss muscular dystrophy, myotonic dystrophy I, mitochondrial myopathies, fatty-acid oxidation defects, and dystrophinopathies. To detect arrhythmias with high risk for sudden cardiac death, patients require close follow-up investigations or an implantable loop recorder. Documentation of severe arrhythmias requires immediate treatment according to established guidelines. CONCLUSIONS: Patients with certain hereditary myopathies carry an increased risk for developing severe supraventricular or ventricular arrhythmias and for dying of sudden cardiac death. Close follow-up and long-term surveillance of the electrocardiogram may prevent fatal complications of arrhythmias in these patients. |
| | |
Authors:
|
Josef Finsterer; Claudia Stöllberger; Hans Keller |
Related Documents
:
|
12033359 - Permanent left atrial tachycardia: radiofrequency catheter ablation through the coronar... 12215729 - Mechanisms underlying the development of atrial arrhythmias in heart failure. 11923049 - Echocardiographic predictors of adverse outcomes in primary pulmonary hypertension. 19243349 - Resolution of atrial thrombosis with heparin in a newborn with atrial flutter. 9584299 - Is the atrial high rate episode diagnostic feature reliable in detecting paroxysmal epi... 10190879 - Right atrial flutter due to lower loop reentry: mechanism and anatomic substrates. 15626269 - Management and outcomes of patients transferred for rescue coronary angioplasty in acut... 442059 - Long term performance of 580 homograft and autograft valves used for aortic valve repla... 20801809 - Bas/bscr17 myocardial xanthine oxidase regulates basal inotropy in murine left ventricu... |
Publication Detail:
|
Type: JOURNAL ARTICLE Date: 2012-3-14 |
Journal Detail:
|
Title: Journal of electrocardiology Volume: - ISSN: 1532-8430 ISO Abbreviation: - Publication Date: 2012 Mar |
Date Detail:
|
Created Date: 2012-3-19 Completed Date: - Revised Date: - |
Medline Journal Info:
|
Nlm Unique ID: 0153605 Medline TA: J Electrocardiol Country: - |
Other Details:
|
Languages: ENG Pagination: - Citation Subset: - |
Copyright Information:
|
Copyright © 2012 Elsevier Inc. All rights reserved. |
Affiliation:
|
Krankenanstalt Rudolfstiftung, Vienna, Austria; Danube University Krems, Krems, Austria. |
Export Citation:
|
APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
|
|
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
Previous Document: Deleterious effects of discography radiocontrast solution on human annulus cell in vitro: changes i...
Next Document: ISMP-Spain questionnaire and strategy for improving good medication practices in the andalusian heal...