Document Detail


Another patient with MECP2 mutation without classic Rett syndrome phenotype.
MedLine Citation:
PMID:  15866439     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Rett syndrome and Angelman syndrome are two neurodevelopmental disorders characterized by partial overlapping features. Rett syndrome is frequently caused by a mutation in methyl-CpG-binding protein (MECP2) gene, localized on chromosome Xq28, whereas Angelman syndrome is frequently caused by different genetic anomalies at chromosome 15q11-q13 (deletions, uniparental disomy, imprinting center mutations, ubiquitin E3 ligase [UBE3A] gene mutations). Recently, some patients with a clinical diagnosis of Angelman syndrome were found to have a mutation in MECP2 gene. This report describes another patient with an Angelman-like phenotype and with an MECP2 mutation.
Authors:
Donatella Milani; Chiara Pantaleoni; Stefano D'Arrigo; Angelo Selicorni; Daria Riva
Related Documents :
15034579 - A previously unidentified mecp2 open reading frame defines a new protein isoform releva...
11112359 - Mutations in activation-induced cytidine deaminase in patients with hyper igm syndrome.
17896309 - The retinal ciliopathies.
12237319 - Mutations in human nonmuscle myosin iia found in patients with may-hegglin anomaly and ...
15266619 - A female with complete lack of müllerian fusion, postaxial polydactyly, and tetralogy ...
16906569 - Patched mutations and hairy skin patches: a new sign in gorlin syndrome.
12825879 - Intractable pruritus associated with insulinoma in the absence of multiple endocrine ne...
10403079 - Transient myeloproliferative disorder (transient leukemia) and hematologic manifestatio...
16235019 - A case of hypoplastic left heart syndrome and bicuspid aortic valve in monochorionic tw...
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Pediatric neurology     Volume:  32     ISSN:  0887-8994     ISO Abbreviation:  Pediatr. Neurol.     Publication Date:  2005 May 
Date Detail:
Created Date:  2005-05-03     Completed Date:  2005-07-08     Revised Date:  2006-05-23    
Medline Journal Info:
Nlm Unique ID:  8508183     Medline TA:  Pediatr Neurol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  355-7     Citation Subset:  IM    
Affiliation:
Pediatric Department, Istituti Clinici di Perfezionamento, University of Milan, Italy.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Angelman Syndrome / genetics*,  physiopathology*
Child, Preschool
Chromosomal Proteins, Non-Histone / genetics*
DNA-Binding Proteins / genetics*
Female
Humans
Methyl-CpG-Binding Protein 2
Phenotype
Point Mutation
Repressor Proteins / genetics*
Rett Syndrome / genetics*,  physiopathology*
Chemical
Reg. No./Substance:
0/Chromosomal Proteins, Non-Histone; 0/DNA-Binding Proteins; 0/MECP2 protein, human; 0/Methyl-CpG-Binding Protein 2; 0/Repressor Proteins

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Pediatric meningosarcoma: clinical evolution and genetic instability.
Next Document:  A family of Emery-Dreifuss muscular dystrophy with extreme difference in severity.