Document Detail


Anonychia and absence/hypoplasia of distal phalanges (Cooks syndrome): report of a second family.
MedLine Citation:
PMID:  7473658     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We describe a second family with four affected members in three successive generations with a rare nail dysplasia syndrome. The syndrome, which was first reported by Cooks et al in 1985, is characterised by bilateral nail hypoplasia of digits 1-3, with absence of nails of digits 4-5 of the hands, and total absence of all toe nails. In addition, there is absence/hypoplasia of the distal phalanges of the hands and feet. Our family confirms this syndrome as a distinct entity with autosomal dominant inheritance.
Authors:
N C Nevin; P S Thomas; D J Eedy; C Shepherd
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of medical genetics     Volume:  32     ISSN:  0022-2593     ISO Abbreviation:  J. Med. Genet.     Publication Date:  1995 Aug 
Date Detail:
Created Date:  1995-12-07     Completed Date:  1995-12-07     Revised Date:  2009-11-18    
Medline Journal Info:
Nlm Unique ID:  2985087R     Medline TA:  J Med Genet     Country:  ENGLAND    
Other Details:
Languages:  eng     Pagination:  638-41     Citation Subset:  IM    
Affiliation:
Regional Genetics Centre, Belfast City Hospital Trust, UK.
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MeSH Terms
Descriptor/Qualifier:
Adult
Female
Foot Deformities, Congenital / genetics*,  radiography
Hand Deformities, Congenital / genetics*,  radiography
Humans
Infant
Male
Middle Aged
Nail Diseases / genetics*
Pedigree
Syndrome
Comments/Corrections

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