Document Detail


Anomalous origin of one pulmonary artery from the ascending aorta.
MedLine Citation:
PMID:  15845161     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We describe the surgical repair in three infants presenting with one pulmonary artery arising from the ascending aorta, the other artery arising normally from the right ventricle via the pulmonary trunk. Repair consisted of reimplantation of the anomalous pulmonary artery to the pulmonary trunk, in association with repair of associated intracardiac malformations. All patients survived the surgical procedures, and were discharged in stable clinical condition. Subsequently, two of the three patients developed stenosis at the surgical anastomosis relatively early after the initial procedure, and underwent reoperation. Although survival after operation is now expected for this malformation, reports of late results are lacking. Larger numbers of operations are needed before we can reach definitive conclusions. The origin of one branch pulmonary artery from the ascending aorta in the presence of a pulmonary valve and main pulmonary artery is a very rare congenital cardiac anomaly. PATIENTS AND METHODS: Between January 1995 and June 2003, 3 infant girls presented with the origin of one branch artery from the ascending aorta, while the other pulmonary artery originated from the pulmonary trunk which was in continuity with the right ventricular outflow tract. The pulmonary artery that arose from the right ventricle was left in 2 and right in 1 patient. RESULTS: At the age 13, 48 and 62 days respectively, the patients underwent surgical repair consisting with reimplantation of the anomalous pulmonary artery branch to the pulmonary trunk in association with repair of intracardiac malformations. There were no hospital deaths. Postoperative complications included: prolonged intubation in two patients (10 and 16 days), low output syndrome in 1 patient, cardiac tamponade in 1 patient and seizures in 1 patient. All patients were discharged in good clinical condition. There have been no late deaths. Subsequently, two of the three patients developed stenosis at the surgical anastomosis relatively early after the initial procedure, and after unsuccessful balloon dilation, underwent surgical reoperation. CONCLUSIONS: Although operative survival is now possible for this malformation, reports of late results are lacking. Two of the three patients developed stenosis at the surgical anastomosis relatively early after surgery. Larger numbers of operations are necessaries to reach definitive conclusions.
Authors:
Vladimiro L Vida; Stephen P Sanders; Tomaso Bottio; Nicola Maschietto; Maurizio Rubino; Ornella Milanesi; Giovanni Stellin
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Cardiology in the young     Volume:  15     ISSN:  1047-9511     ISO Abbreviation:  Cardiol Young     Publication Date:  2005 Apr 
Date Detail:
Created Date:  2005-04-22     Completed Date:  2005-09-22     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9200019     Medline TA:  Cardiol Young     Country:  England    
Other Details:
Languages:  eng     Pagination:  176-81     Citation Subset:  IM    
Affiliation:
Department of Pediatric Cardiac Surgery, University of Padova Medical School, 35128 Padova, Italy. vladimirovida@interfree.it
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / surgery*
Aorta / abnormalities*,  surgery*
Follow-Up Studies
Humans
Infant
Infant, Newborn
Pulmonary Artery / abnormalities*,  surgery*
Reoperation

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