Document Detail


Anomalies of the fingers and toes associated with Klippel-Trenaunay syndrome.
MedLine Citation:
PMID:  1660897     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Klippel-Trenaunay syndrome is a rare congenital malformation characterized by a large angiomatous nevus; hypertrophy of soft tissue or overgrowth of bone, or both; and venous varicosities. The cases of 108 patients who had a diagnosis of this syndrome between 1956 and 1990 were reviewed. One hundred and twenty-six anomalies were found in twenty-nine patients, each of whom had one to thirteen malformations of the fingers or toes, or both. The ratio of female patients to male patients was approximately two to one. Twenty-six patients had macrodactyly affecting one to six digits; nine, syndactyly involving two or more digits; five, metatarsus primus varus; two, clinodacytly; two, polydactyly; one, camptodactyly; and one, a congenital trigger finger. Thirty-three of the 126 anomalies were in extremities that had no nevi, varicose veins, or generalized hypertrophy.
Authors:
B J McGrory; P C Amadio; J H Dobyns; G B Stickler; K K Unni
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  The Journal of bone and joint surgery. American volume     Volume:  73     ISSN:  0021-9355     ISO Abbreviation:  J Bone Joint Surg Am     Publication Date:  1991 Dec 
Date Detail:
Created Date:  1992-01-23     Completed Date:  1992-01-23     Revised Date:  2010-10-25    
Medline Journal Info:
Nlm Unique ID:  0014030     Medline TA:  J Bone Joint Surg Am     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  1537-46     Citation Subset:  AIM; IM    
Affiliation:
Department of Orthopedics, Mayo Clinic, Rochester, Minnesota 55905.
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Adult
Child
Child, Preschool
Female
Fingers / abnormalities*
Foot Deformities, Congenital / complications
Hand Deformities, Congenital / complications
Humans
Infant
Klippel-Trenaunay-Weber Syndrome / complications*,  pathology
Male
Skin / pathology
Syndactyly / complications
Toes / abnormalities*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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