| Angiosarcoma of the liver in childhood: a clinicopathologic and follow-up study of 10 cases. | |
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MedLine Citation:
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PMID: 1409148 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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The clinical, morphologic, and follow-up findings in 10 cases of childhood hepatic angiosarcoma are reported. Six patients were female and four were male. The age range was 18 months to 7 years, with a mean of 3.7 years. The usual presenting feature was an abdominal mass, with or without associated symptoms. The histologic pattern of childhood hepatic angiosarcoma typically consists of large hypercellular whorls of spindled sarcoma cells intermingled with bile ducts, vessels, and collagen. Factor VIII staining of tumor cells is focal, cytoplasmic, and weak in character. Intracellular eosinophilic, PAS-positive globules are present in most cases and may be abundant. The prognosis is poor; follow-up available in seven cases showed only one to be alive 32 months after diagnosis. The remaining six patients had died 0-27 months (mean 10 months) after diagnosis. |
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Authors:
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D M Selby; J T Stocker; K G Ishak |
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Publication Detail:
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Type: Journal Article; Research Support, Non-U.S. Gov't; Review |
Journal Detail:
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Title: Pediatric pathology / affiliated with the International Paediatric Pathology Association Volume: 12 ISSN: 0277-0938 ISO Abbreviation: Pediatr Pathol Publication Date: 1992 Jul-Aug |
Date Detail:
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Created Date: 1992-11-10 Completed Date: 1992-11-10 Revised Date: 2006-11-15 |
Medline Journal Info:
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Nlm Unique ID: 8303527 Medline TA: Pediatr Pathol Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 485-98 Citation Subset: IM |
Affiliation:
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Department of Pediatric Pathology, Armed Forces Institute of Pathology, Washington, D.C. 20306. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Adrenal Gland Neoplasms
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secondary Child Child, Preschool Female Follow-Up Studies Hemangiosarcoma / pathology*, secondary, therapy, ultrastructure Humans Infant Kidney Neoplasms / secondary Liver Neoplasms / pathology*, therapy, ultrastructure Lung Neoplasms / secondary Male Microscopy, Electron |
| Comments/Corrections | |
Comment In:
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Pediatr Pathol. 1993 Jul-Aug;13(4):541-5
[PMID:
8372037
]
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From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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