| Angiomatosis osteohypotrophica. | |
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MedLine Citation:
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PMID: 7112039 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Based on a clinical and radiological study of seven patients, a syndrome consisting of congenital hemangiomas with arteriovenous fistulae engaging the soft tissues and the bones, and associated with shortening of the involved extremity, for which we suggest the name angiomatosis osteohypotrophica, is reported. Angioma, varicose veins and/or arteriovenous fistulae with resulting increase in limb have been widely known since the beginning of this century as Klippel-Trénaunay syndrome. Although the patients in this series present all other features of Klippel-Trénaunay syndrome, thinning and shortening of the long bones occurred, resulting in an overall reduction in limb length. Intraosseous hemangiomas in the metacarpal, respective metatarsal bones were common characteristic findings. The arteriograms undertaken in this study showed, in addition to hemangiomas, presence of arteriovenous shunts within the area of the tumour. Their influence on skeletal growth is discussed. |
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Authors:
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I A Niechajev; S Karlsson |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Scandinavian journal of plastic and reconstructive surgery Volume: 16 ISSN: 0036-5556 ISO Abbreviation: Scand J Plast Reconstr Surg Publication Date: 1982 |
Date Detail:
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Created Date: 1982-10-21 Completed Date: 1982-10-21 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 0121375 Medline TA: Scand J Plast Reconstr Surg Country: SWEDEN |
Other Details:
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Languages: eng Pagination: 77-85 Citation Subset: IM |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Adolescent Adult Angiomatosis / complications*, radiography Arteriovenous Malformations / complications Bone Diseases, Developmental / complications*, radiography Child Female Hemangioma / complications Humans Male Syndrome |
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