Document Detail


Angioedema with normal C1q and C1 inhibitor: an atypical presentation of Waldenström macroglobulinemia.
MedLine Citation:
PMID:  23591717     Owner:  NLM     Status:  Publisher    
Abstract/OtherAbstract:
Angioedema is a recurrent, non-pitting, non-pruritic, transitory swelling due to transient increase of endothelial permeability in the capillaries of the deep cutaneous and mucosal layers. Angioedema is generally categorized based on etiology, and characteristic lab findings are associated with each category. Cases of acquired angioedema associated with myeloproliferative disorders have been described in the literature, but these have been associated with a characteristic low C1q, a defining laboratory finding in acquired angioedema. Here we present a case of 68-year-old female with acquired angioedema that was not associated with low C1q, but was found to have Waldenström disease. Her angioedema responded dramatically to combination therapy consisting of bortezomib, rituximab, and dexamethasone.
Authors:
Anas Khanfar; Anita Trikha; Rana Bonds; Bagi Jana
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Publication Detail:
Type:  JOURNAL ARTICLE     Date:  2013-4-17
Journal Detail:
Title:  International journal of hematology     Volume:  -     ISSN:  1865-3774     ISO Abbreviation:  Int. J. Hematol.     Publication Date:  2013 Apr 
Date Detail:
Created Date:  2013-4-17     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9111627     Medline TA:  Int J Hematol     Country:  -    
Other Details:
Languages:  ENG     Pagination:  -     Citation Subset:  -    
Affiliation:
Department of Internal Medicine, University of Texas Medical Branch, 301 University Blvd, Galveston, TX, 77555, USA, akhanfer2003@yahoo.co.uk.
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