| Aneurysmatic dilatation of ascending aorta in a patient with beta-thalassemia and a pseudoxanthoma elasticum-like syndrome. | |
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MedLine Citation:
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PMID: 15014899 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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The development of a diffuse elastic tissue defect resembling pseudoxanthoma elasticum (PXE) is a recently established and frequently encountered clinical entity in beta-thalassemia. The clinical spectrum of this disorder is not yet completely understood as it is continuously being enriched with novel complications that are often serious. We present here a thalassemia intermedia patient with typical PXE manifestations and a fusiform aneurysmatic dilatation of the ascending thoracic aorta, a previously unknown complication in these patients. An aortic aneurysm has itself a notable morbidity, while it may also impair the particularly susceptible cardiac function of beta-thalassemia patients, hence affecting the overall prognosis of the main disease. |
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Authors:
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Dimitrios Farmakis; Vassiliki Vesleme; Argiroula Papadogianni; Panagiotis Tsaftaridis; Pantelis Kapralos; Athanasios Aessopos |
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Publication Detail:
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Type: Case Reports; Journal Article Date: 2004-03-11 |
Journal Detail:
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Title: Annals of hematology Volume: 83 ISSN: 0939-5555 ISO Abbreviation: Ann. Hematol. Publication Date: 2004 Sep |
Date Detail:
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Created Date: 2004-09-27 Completed Date: 2004-10-20 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 9107334 Medline TA: Ann Hematol Country: Germany |
Other Details:
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Languages: eng Pagination: 596-9 Citation Subset: IM |
Affiliation:
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First Department of Internal Medicine, University of Athens, Medical School, Laiko General Hospital, Athens, Greece. dfarm1@panafonet.gr |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adult Aorta / pathology* Dilatation, Pathologic / complications*, pathology* Female Humans Pseudoxanthoma Elasticum / complications* Syndrome Tomography, Emission-Computed beta-Thalassemia / complications*, therapy |
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