Document Detail

Anesthetic management of a patient with Cri Du Chat syndrome. Case report.
MedLine Citation:
PMID:  21146059     Owner:  NLM     Status:  MEDLINE    
BACKGROUND AND OBJECTIVES: Cri Du Chat syndrome is a chromosomal disorder with peculiar clinical characteristics including airways abnormalities that require special care by anesthesiologists when handling those patients.
OBJECTIVE: To present a case of outpatient anesthesia in a patient with Cri Du Chat syndrome and discuss the anesthetic aspects related to this disorder.
CASE REPORT: Male patient, 14 years old, 25 kg, with Cri Du Chat syndrome, physical status ASA P2, was admitted for upper gastrointestinal endoscopy and esophageal dilation. The patient had mental retardation, a few episodes of seizures, and marked hypertonia of the limbs. Airways exam showed limited cervical mobility and thyromental distance less than six centimeters. The patient was unable to comprehend verbal commands, making it difficult to undertake a complete assessment of the airways. Other findings on physical exam included microcephaly, micrognathism, subtle strabismus, limb hypertonia with flexion, and protrusion of the tip of the tongue. Intravenous fentanyl 50 μg, midazolam 1 mg, and propofol 60 mg were administered. The patient was maintained on spontaneous ventilation. The procedure lasted 5 minutes, without intercurrences.
CONCLUSIONS: Patients with Cri Du Chat syndrome have clinical characteristics that are very important for their anesthetic management, being the responsibility of the anesthesiologist to consider carefully the structural particularities of each patient.
Klaus Morales dos Santos; Daniel Câmara de Rezende; Ziltomar Donizetti de Oliveira Borges
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Revista brasileira de anestesiologia     Volume:  60     ISSN:  1806-907X     ISO Abbreviation:  Rev Bras Anestesiol     Publication Date:    2010 Nov-Dec
Date Detail:
Created Date:  2010-12-14     Completed Date:  2011-06-06     Revised Date:  2014-02-05    
Medline Journal Info:
Nlm Unique ID:  0401316     Medline TA:  Rev Bras Anestesiol     Country:  Brazil    
Other Details:
Languages:  eng; por     Pagination:  630-3, 350-1     Citation Subset:  IM    
Copyright Information:
© 2010 Elsevier Editora Ltda. All rights reserved.
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MeSH Terms
Anesthesia / methods*
Cri-du-Chat Syndrome*
Risk Factors

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

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