| Anesthetic management of a patient with Alport-leiomyomatosis syndrome. | |
| | |
MedLine Citation:
|
PMID: 19685135 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
|
We report the anesthetic management of esophagectomy for a patient with Alport-leiomyomatosis syndrome. A 23-year-old woman complained of dysphagia and severe chest pain. Her chest X-ray, computed tomography (CT), and magnetic resonance imaging (MRI) showed an enlarged esophagus, in contact with the trachea, heart, aorta, and large vessels. She frequently experienced severe asthma attacks. Because various risks in both respiration and circulation, especially in anesthesia induction, were of concern, her right femoral vessels were exposed, for the emergency use of percutaneous cardiopulmonary support (PCPS), prior to anesthesia induction. Anesthesia was induced and maintained with propofol, fentanyl, and vecuronium. Esophagectomy was performed uneventfully and no severe events were seen in anesthesia management. Alportleiomyomatosis syndrome is a very rare disease. When we are involved in the anesthetic management of a patient with this disease, evaluation of the influence of the enlarged esophagus on both respiration and circulation, and careful preparation for emergence, are very important. |
| | |
Authors:
|
Motohiko Hanazaki; Ken Takata; Keiji Goto; Hiroshi Katayama; Masataka Yokoyama; Kiyoshi Morita; Yasuhiro Shirakawa; Tomoki Yamatsuji; Yoshio Naomoto |
Related Documents
:
|
290805 - Myofacial pain dysfunction: a manifestation of the short-face syndrome. 7769945 - Usher's syndrome type 3 in finland. 7063695 - 99mtc-hida cholescintigraphy in dubin-johnson and rotor syndromes. 22323985 - Pathophysiologic findings of irritable bowel syndrome in china. 10818855 - Prader willi and angelman syndromes: exemplars of genomic imprinting. 2018065 - Simpson-golabi-behmel syndrome with severe cardiac arrhythmias. |
Publication Detail:
|
Type: Case Reports; Journal Article Date: 2009-08-14 |
Journal Detail:
|
Title: Journal of anesthesia Volume: 23 ISSN: 1438-8359 ISO Abbreviation: J Anesth Publication Date: 2009 |
Date Detail:
|
Created Date: 2009-08-17 Completed Date: 2009-12-07 Revised Date: - |
Medline Journal Info:
|
Nlm Unique ID: 8905667 Medline TA: J Anesth Country: Japan |
Other Details:
|
Languages: eng Pagination: 453-5 Citation Subset: IM |
Affiliation:
|
Department of Anesthesiology and Resuscitology, Okayama University Medical School, 2-5-1 Shikata-cho, Okayama 700-8558, Japan. |
Export Citation:
|
APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
|
Anesthesia, General* Asthma / complications Esophageal Neoplasms / complications*, pathology, radiography Esophagectomy* Female Forced Expiratory Volume Humans Leiomyomatosis / complications*, pathology, radiography Magnetic Resonance Imaging Syndrome Tomography, X-Ray Computed Young Adult |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
Previous Document: Volume manipulation by phlebotomy for cesarean section in a patient with pulmonary hypertension.
Next Document: Anesthetic management of a child with Langer-Giedion (TRPS II) syndrome.