| Anesthetic management of an adult patient with Cornelia de Lange Syndrome. | |
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MedLine Citation:
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PMID: 20203551 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Cornelia de Lange Syndrome is a well-known congenital disease characterized by multiple malformations that make anesthetic management a challenge. Since few individuals survive the earliest stage of life, papers describing the details of anesthetic management are mainly reported in the pediatric population. These individuals who move into adulthood develop physical changes that should be taken into consideration. This article reports the case of a 34-year-old patient undergoing an orthopedic procedure. The operation was performed under general anesthesia because the patient showed severe scoliosis and joint contractures, so extraordinary difficulty in neuroaxial and peripheral techniques was expected. The aggressive behavior of the patient impeded the proper assessment of a preoperative airway. Fiber optic intubation was performed under slight sedation after three unsuccessful attempts. Dental crowding, prominent upper central incisors that were more pronounced than in most children, a short and stiff neck, and poor patient cooperation due to mental retardation and occasional autistic behavior made airway management difficult. This case should alert anesthesiologists to the greater difficulties of managing patients with Cornelia de Lange Syndrome when they become adults. |
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Authors:
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M D Torres; E Calvo; F Fern?ndez Espl?; F Gilsanz |
Publication Detail:
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Type: Case Reports; Journal Article Date: 2010-02-05 |
Journal Detail:
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Title: Minerva anestesiologica Volume: 76 ISSN: 1827-1596 ISO Abbreviation: Minerva Anestesiol Publication Date: 2010 Mar |
Date Detail:
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Created Date: 2010-03-05 Completed Date: 2010-05-25 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 0375272 Medline TA: Minerva Anestesiol Country: Italy |
Other Details:
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Languages: eng Pagination: 229-31 Citation Subset: IM |
Affiliation:
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Department of Anesthesiology, Hospital la Paz, Paseo de la Castellana 261, Madrid, Spain. mdoltorr@yahoo.es |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adult Anesthesia, General* De Lange Syndrome / surgery* Humans Intubation, Intratracheal Male Orthopedic Procedures |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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