| Anaesthetic management of Osler-Weber-Rendu syndrome with coexisting congenital methaemoglobinaemia. | |
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MedLine Citation:
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PMID: 16146483 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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A 9-year-old cyanosed child suffering from Osler-Weber-Rendu syndrome with bilateral pulmonary arteriovenous malformations (PAVMs) was posted for cerebral angiography under general anaesthesia. Careful preanaesthetic evaluation led to the diagnosis of coexisting congenital methaemoglobinaemia. There is no previous report of Osler-Weber-Rendu syndrome coexisting with congenital methaemoglobinaemia. This report emphasizes that a second contributory cause of cyanosis must be suspected and meticulously looked for if the symptomatology in a patient cannot be explained by a single established diagnosis. Positive-pressure ventilation was associated with reduction in arterial oxygenation despite an increasing inspired oxygen concentration, which returned to preanaesthetic levels only after extubation and resumption of spontaneous respiration. |
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Authors:
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D Sharma; M P Pandia; P K Bithal |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Acta anaesthesiologica Scandinavica Volume: 49 ISSN: 0001-5172 ISO Abbreviation: Acta Anaesthesiol Scand Publication Date: 2005 Oct |
Date Detail:
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Created Date: 2005-09-08 Completed Date: 2005-12-15 Revised Date: 2007-11-15 |
Medline Journal Info:
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Nlm Unique ID: 0370270 Medline TA: Acta Anaesthesiol Scand Country: Denmark |
Other Details:
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Languages: eng Pagination: 1391-4 Citation Subset: IM |
Affiliation:
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Department of Neuroanaesthesiology, Neurosciences Centre, All India Institute of Medical Sciences, New Delhi, India. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Anesthesia* Anesthesia, General Blood Gas Analysis Cerebral Angiography Child Consanguinity Cyanosis / complications Hemodynamics Humans Lung / radiography Male Methemoglobinemia / complications*, congenital* Telangiectasia, Hereditary Hemorrhagic / complications* |
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