Document Detail


Anaesthetic implications of LEOPARD syndrome.
MedLine Citation:
PMID:  15078383     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
LEOPARD syndrome is a neuroectodermal disorder presumed to result from an abnormality in neural crest cells. The acronym 'LEOPARD' is derived from the clinical features which include multiple lentigines, electrocardiographic abnormalities, ocular hypertelorism, pulmonary stenosis, abnormal genitalia, retarded growth, and deafness. Given the multisystem nature of the disease process, several issues may affect the perioperative care of these patients. Of primary importance are associated conditions of the cardiovascular system including congenital heart disease, conduction disturbances, and progressive hypertrophic obstructive cardiomyopathy. The authors present a 4-year old boy who presented for anaesthetic care for repair of a ventricular septal defect and pulmonary valvotomy for congenital pulmonary stenosis. The potential perioperative implications of LEOPARD syndrome are discussed.
Authors:
Javier Torres; Pierantonio Russo; Joseph D Tobias
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Paediatric anaesthesia     Volume:  14     ISSN:  1155-5645     ISO Abbreviation:  Paediatr Anaesth     Publication Date:  2004 Apr 
Date Detail:
Created Date:  2004-04-13     Completed Date:  2004-07-22     Revised Date:  2004-12-24    
Medline Journal Info:
Nlm Unique ID:  9206575     Medline TA:  Paediatr Anaesth     Country:  France    
Other Details:
Languages:  eng     Pagination:  352-6     Citation Subset:  IM    
Affiliation:
The Department of Child Health, The Division of Pediatric Critical Care/Pediatric Anesthesiology, The University of Missouri, Columbia, MO 65212, USA.
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MeSH Terms
Descriptor/Qualifier:
Anesthesia, General / methods*
Anesthetics, Inhalation / administration & dosage
Anesthetics, Intravenous / administration & dosage
Atracurium / administration & dosage,  analogs & derivatives*
Cardiopulmonary Bypass
Child, Preschool
Fentanyl / administration & dosage
Heart Septal Defects, Ventricular / surgery
Humans
LEOPARD Syndrome / physiopathology*
Male
Methyl Ethers / administration & dosage
Neuromuscular Blocking Agents / administration & dosage
Perioperative Care
Pulmonary Valve / surgery
Pulmonary Valve Stenosis / congenital,  surgery
Chemical
Reg. No./Substance:
0/Anesthetics, Inhalation; 0/Anesthetics, Intravenous; 0/Methyl Ethers; 0/Neuromuscular Blocking Agents; 0/cisatracurium; 28523-86-6/sevoflurane; 437-38-7/Fentanyl; 64228-79-1/Atracurium

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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