Document Detail


Alternative modes of GM-CSF receptor activation revealed using activated mutants of the common beta-subunit.
MedLine Citation:
PMID:  20173116     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Granulocyte/macrophage colony-stimulating factor promotes growth, survival, differentiation, and activation of normal myeloid cells and plays an important role in myeloid leukemias. The GM-CSF receptor (GMR) shares a signaling subunit, beta(c), with interleukin-3 and interleukin-5 receptors and has recently been shown to induce activation of Janus kinase 2 (JAK2) and downstream signaling via formation of a unique dodecameric receptor complex. In this study we use 2 activated beta(c) mutants that display distinct signaling capacity and have differential requirements for the GMR alpha-subunit (GMR-alpha) to dissect the signaling pathways associated with the GM-CSF response. The V449E transmembrane mutant selectively activates JAK2/signal transducer and activator of transcription 5 and extracellular signal-regulated kinase (ERK) pathways, resulting in a high level of sensitivity to JAK and ERK inhibitors, whereas the extracellular mutant (FIDelta) selectively activates the phosphoinositide 3-kinase/Akt and IkappaKbeta/nuclear factorkappaB pathways. We also demonstrate a novel and direct interaction between the SH3 domains of Lyn and Src with a conserved proline-rich motif in GMR-alpha and show a selective requirement for Src family kinases by the FIDelta mutant. We relate the nonoverlapping nature of signaling by the activated mutants to the structure of the unique GMR complex and propose alternative modes of receptor activation acting synergistically in the mature liganded receptor complex.
Authors:
Michelle Perugini; Anna L Brown; Diana G Salerno; Grant W Booker; Cvetan Stojkoski; Timothy R Hercus; Angel F Lopez; Margaret L Hibbs; Thomas J Gonda; Richard J D'Andrea
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Publication Detail:
Type:  Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't     Date:  2010-02-19
Journal Detail:
Title:  Blood     Volume:  115     ISSN:  1528-0020     ISO Abbreviation:  Blood     Publication Date:  2010 Apr 
Date Detail:
Created Date:  2010-04-23     Completed Date:  2010-05-20     Revised Date:  2011-07-28    
Medline Journal Info:
Nlm Unique ID:  7603509     Medline TA:  Blood     Country:  United States    
Other Details:
Languages:  eng     Pagination:  3346-53     Citation Subset:  AIM; IM    
Affiliation:
Division of Haematology, Centre for Cancer Biology, SA Pathology, Adelaide, Australia.
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MeSH Terms
Descriptor/Qualifier:
Animals
Blotting, Western
Cell Line
Enzyme Activation / physiology*
Flow Cytometry
Immunoprecipitation
Leukemia, Myeloid, Acute / metabolism
Mice
Microscopy, Fluorescence
Mutation
Receptors, Granulocyte-Macrophage Colony-Stimulating Factor / metabolism*
Signal Transduction / physiology*
Grant Support
ID/Acronym/Agency:
R01 HL60657/HL/NHLBI NIH HHS
Chemical
Reg. No./Substance:
0/Receptors, Granulocyte-Macrophage Colony-Stimulating Factor
Comments/Corrections

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