Document Detail


Algodystrophy in conjunction with van der Hoeve's syndrome.
MedLine Citation:
PMID:  7554566     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Van der Hoeve's syndrome is the all-round variant of Lobstein's disease (late osteogenesis imperfecta) and is characterized by the concurrent presence of osteoporosis, blue sclerae, and deafness. The literature has reported sporadic cases of a combination of algodystrophic syndrome and Lobstein's disease. Our case represents a classic example: a 50-year-old woman with blue sclerae since birth, bilateral deafness, major dental alterations, vitreous osteoporosis and a history of pathological fractures who, two years from the onset of menopause, complained of pain involving the right ankle. After admission to our Department, a diagnosis of algodystrophy combined with van der Hoeve's syndrome was made on the basis of her clinical history, objective signs and x-ray results. Treatment consisted of i.v. clodronate disodium at a dose of 300 mg daily in 250 ml saline solution for 7 consecutive days. At the end of the treatment cycle the patient reported an improvement in her symptoms with nearly total regression of right ankle pain, while swelling disappeared within a few weeks.
Authors:
G Chérié-Lignière; U Tamborini; P Grosso
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Clinical and experimental rheumatology     Volume:  13     ISSN:  0392-856X     ISO Abbreviation:  Clin. Exp. Rheumatol.     Publication Date:    1995 May-Jun
Date Detail:
Created Date:  1995-11-13     Completed Date:  1995-11-13     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  8308521     Medline TA:  Clin Exp Rheumatol     Country:  ITALY    
Other Details:
Languages:  eng     Pagination:  361-5     Citation Subset:  IM    
Affiliation:
Department of Systemic and Local Treatment of Chronic Inflammatory Rheumatism, G. Pini Orthopaedics Institute, Milan, Italy.
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MeSH Terms
Descriptor/Qualifier:
Clodronic Acid / administration & dosage
Female
Humans
Infusions, Intravenous
Middle Aged
Osteogenesis Imperfecta / complications*,  drug therapy
Reflex Sympathetic Dystrophy / complications*,  drug therapy
Chemical
Reg. No./Substance:
10596-23-3/Clodronic Acid

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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