Document Detail


Albright's hereditary osteodystrophy with extensive heterotopic ossification of the oral and maxillofacial region: how fetuin research may help a seemingly impossible condition.
MedLine Citation:
PMID:  18028761     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Albright"s hereditary osteodystrophy (AHO) is a complex genetic disorder characterized by brachydactyly, gonadotropin resistance, hypothyroidism, pseudohypoparathyroid syndrome and heterotopic ossification. Heterotopic ossification rarely occurs in the maxillofacial region. In this article, we present such a case, describe the etiology, characteristics and treatment of AHO and suggest a potential role of an inhibitor of bone formation such as fetuin in preventing recurrence of aberrant ossification.
Authors:
Marc G DuVal; Sarah Davidson; Andrew Ho; Rachale Cohen; Michael Park; Somayeh Nourian; Gerald Baker; George K B Sándor
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal (Canadian Dental Association)     Volume:  73     ISSN:  1488-2159     ISO Abbreviation:  J Can Dent Assoc     Publication Date:  2007 Nov 
Date Detail:
Created Date:  2007-11-21     Completed Date:  2007-12-12     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  7907605     Medline TA:  J Can Dent Assoc     Country:  Canada    
Other Details:
Languages:  eng     Pagination:  845-50     Citation Subset:  D; IM    
Affiliation:
Mount Sinai Hospital, Toronto, Ontario, Canada.
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Ankylosis / etiology
Bone Morphogenetic Proteins / metabolism
Fibrous Dysplasia, Polyostotic / complications*
Humans
Male
Masticatory Muscles / physiopathology
Maxillofacial Abnormalities / etiology*
Ossification, Heterotopic / etiology*,  prevention & control
Osteogenesis / physiology
Pseudopseudohypoparathyroidism / complications*
Temporomandibular Joint Disorders / etiology
Transforming Growth Factor beta1 / metabolism
alpha-Fetoproteins / physiology*
Chemical
Reg. No./Substance:
0/Bone Morphogenetic Proteins; 0/Transforming Growth Factor beta1; 0/alpha-Fetoproteins

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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