| The Alagille's syndrome and its anaesthetic considerations. | |
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MedLine Citation:
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PMID: 9483604 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Alagille's syndrome is an inherited disorder affecting multiple organ systems. Most characteristic is the paucity of the interlobular bile ducts with cholestasis. The anaesthetic plan for these patients should be based on careful preoperative preparation and attention to the issues involving hepatobiliary, cardiac, neurodevelopmental, nutritional, haematological, ocular and facial abnormalities. We report the case of a five-and-a-half-year old patient with Alagille's syndrome who sustained a pathological fracture of the femur and was scheduled for closed reduction and application of a hip spica cast. Relevant anaesthetic issues are discussed. |
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Authors:
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D K Choudhry; M A Rehman; R E Schwartz; D A Piccoli |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Paediatric anaesthesia Volume: 8 ISSN: 1155-5645 ISO Abbreviation: Paediatr Anaesth Publication Date: 1998 |
Date Detail:
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Created Date: 1998-04-09 Completed Date: 1998-04-09 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 9206575 Medline TA: Paediatr Anaesth Country: FRANCE |
Other Details:
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Languages: eng Pagination: 79-82 Citation Subset: IM |
Affiliation:
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Department of Anaesthesia and Critical Care, St. Christopher's Hospital for Children, Philadelphia, PA 19134-1095, USA. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Alagille Syndrome* Anesthesia / methods* Child, Preschool Female Humans |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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